Diagnosis Code

Q26.4 ANOMALOUS PULMONARY VENOUS CONNECTION, UNSPECIFIED


Code Information

Diagnosis Code: Q26.4

Short Description: Anomalous pulmonary venous connection, unspecified

Long Description: Anomalous pulmonary venous connection, unspecified

The code Q26.4 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations of the circulatory system (Q20-Q28)
      • Congenital malformations of great veins (Q26)
        • Q26.4 Anomalous pulmonary venous connection, unspecified

Code Version: 2022 ICD-10-CM


Synonyms

  • Abnormal inferior vena caval connection
  • Anomalous pulmonary to systemic collateral vein
  • Anomalous pulmonary venous connection of mixed type
  • Anomalous pulmonary venous connection of mixed type with two pulmonary venous confluences
  • Anomalous pulmonary venous drainage
  • Anomalous pulmonary venous drainage to abdominal portion of inferior vena cava
  • Anomalous pulmonary venous drainage to coronary sinus
  • Anomalous pulmonary venous drainage to hepatic veins
  • Anomalous pulmonary venous drainage to right atrium
  • Anomalous pulmonary venous drainage to superior vena cava
  • Anomalous termination of right pulmonary vein
  • Congenital abnormality of hepatic vein
  • Congenital hypoplasia of pulmonary artery
  • Congenital pulmonary vein confluence
  • Cor triatriatum with some pulmonary veins to proximal chamber draining to left atrium
  • Cor triatriatum with some pulmonary veins to proximal chamber draining to right atrium and others connecting directly to left atrium
  • Divided left atrium with some pulmonary veins to proximal chamber
  • Divided left atrium with some pulmonary veins to proximal chamber
  • Divided left atrium with some pulmonary veins to proximal chamber
  • Divided left atrium with some pulmonary veins to proximal chamber draining to left atrium and others connecting directly to left atrium
  • Divided left atrium with some pulmonary veins to proximal chamber draining to right atrium
  • Divided left atrium with some pulmonary veins to proximal chamber draining to right atrium
  • Divided left atrium with some pulmonary veins to proximal chamber draining to right atrium and others connecting anomalously
  • Infracardiac location of anomalous pulmonary venous connection
  • Infracardiac location of anomalous pulmonary venous connection to hepatic vein
  • Infracardiac location of anomalous pulmonary venous connection to patent venous duct
  • Infracardiac location of anomalous pulmonary venous connection with two descending veins
  • Infracardiac location of anomalous pulmonary venous connections to inferior caval vein
  • Infracardiac location of anomalous pulmonary venous connections to portal system
  • Intracardiac location of anomalous pulmonary venous connection
  • Intracardiac location of anomalous pulmonary venous connection to coronary sinus
  • Intracardiac location of anomalous pulmonary venous connection to midline with isomeric atria
  • Intracardiac location of anomalous pulmonary venous connection to right atrium
  • Intracardiac location of anomalous pulmonary venous connections to bilateral isomeric atriums
  • Obstructed pulmonary venous connection
  • Obstructed pulmonary venous connection at coronary sinus orifice
  • Pulmonary vein atresia
  • Pulmonary venous confluence in direct proximity to left atrium
  • Pulmonary venous confluence in horizontal orientation
  • Pulmonary venous confluence in vertical orientation
  • Pulmonary venous confluence remote from left atrium
  • Scimitar syndrome
  • Scimitar syndrome with additional anomalous pulmonary venous connection
  • Supracardiac location of anomalous pulmonary venous connection
  • Supracardiac location of anomalous pulmonary venous connection to azygos vein
  • Supracardiac location of anomalous pulmonary venous connection to hemiazygos vein
  • Supracardiac location of anomalous pulmonary venous connection to left sided vertical vein
  • Supracardiac location of anomalous pulmonary venous connection to left superior caval vein
  • Supracardiac location of anomalous pulmonary venous connection to right sided vertical vein
  • Supracardiac location of anomalous pulmonary venous connection to right superior caval vein
  • Transposition of pulmonary veins

Diagnostic Related Group(s)

The code Q26.4 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Cardiac Congenital And Valvular Disorders With Mcc (306)
  • Cardiac Congenital And Valvular Disorders Without Mcc (307)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q26.4 Right Arrow 747.42 Part anom pulm ven conn

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q26 Congenital malformations of great veins
Q26.0 Congenital stenosis of vena cava
Q26.1 Persistent left superior vena cava
Q26.2 Total anomalous pulmonary venous connection
Q26.3 Partial anomalous pulmonary venous connection
Q26.5 Anomalous portal venous connection
Q26.6 Portal vein-hepatic artery fistula
Q26.8 Other congenital malformations of great veins
Q26.9 Congenital malformation of great vein, unspecified


This page was last updated on: 10/1/2023