Diagnosis Code

Q80.1 X-LINKED ICHTHYOSIS


Code Information

Diagnosis Code: Q80.1

Short Description: X-linked ichthyosis

Long Description: X-linked ichthyosis

The code Q80.1 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Congenital ichthyosis (Q80)
        • Q80.1 X-linked ichthyosis

Code Version: 2022 ICD-10-CM


Synonyms

  • Autosomal dominant ichthyosis
  • Deficiency of steryl-sulfatase
  • Deficiency of steryl-sulfatase
  • Syndromic recessive X-linked ichthyosis
  • X-linked ichthyosis with steryl-sulfatase deficiency
  • X-linked ichthyosis with steryl-sulfatase deficiency

Diagnostic Related Group(s)

The code Q80.1 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Minor Skin Disorders With Mcc (606)
  • Minor Skin Disorders Without Mcc (607)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q80.1 Right Arrow 757.1 Ichthyosis congenita

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q80 Congenital ichthyosis
Q80.0 Ichthyosis vulgaris
Q80.2 Lamellar ichthyosis
Q80.3 Congenital bullous ichthyosiform erythroderma
Q80.4 Harlequin fetus
Q80.8 Other congenital ichthyosis
Q80.9 Congenital ichthyosis, unspecified


This page was last updated on: 10/1/2023