Diagnosis Code

Q89.01 ASPLENIA (CONGENITAL)


Code Information

Diagnosis Code: Q89.01

Short Description: Asplenia (congenital)

Long Description: Asplenia (congenital)

The code Q89.01 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Other congenital malformations, not elsewhere classified (Q89)
        • Q89.01 Asplenia (congenital)

Code Version: 2022 ICD-10-CM


Synonyms

  • Agenesis of spleen
  • Aplasia of spleen
  • Asplenia
  • Asplenia
  • Asplenia
  • Congenital absence of spleen
  • Congenital absence of spleen
  • Congenital diaphragmatic hernia
  • Congenital miosis
  • Congenital short bowel syndrome
  • Constricted pupil
  • Diaphragmatic hernia, short bowel, asplenia syndrome
  • Familial isolated congenital asplenia
  • Functional asplenia
  • Short bowel syndrome
  • Spleen absent
  • Thrombocytopathy, asplenia and miosis

Diagnostic Related Group(s)

The code Q89.01 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Reticuloendothelial And Immunity Disorders With Mcc (814)
  • Reticuloendothelial And Immunity Disorders With Cc (815)
  • Reticuloendothelial And Immunity Disorders Without Cc/mcc (816)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q89.01 Right Arrow 759.0 Anomalies of spleen

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q89 Other congenital malformations, not elsewhere classified
Q89.0 Congenital absence and malformations of spleen
Q89.09 Congenital malformations of spleen
Q89.1 Congenital malformations of adrenal gland
Q89.2 Congenital malformations of other endocrine glands
Q89.3 Situs inversus
Q89.4 Conjoined twins
Q89.7 Multiple congenital malformations, not elsewhere classified
Q89.8 Other specified congenital malformations
Q89.9 Congenital malformation, unspecified


This page was last updated on: 10/1/2023