Diagnosis Code

Q89.3 SITUS INVERSUS


Code Information

Diagnosis Code: Q89.3

Short Description: Situs inversus

Long Description: Situs inversus

The code Q89.3 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Other congenital malformations, not elsewhere classified (Q89)
        • Q89.3 Situs inversus

Code Version: 2022 ICD-10-CM


Synonyms

  • Agnathia, holoprosencephaly, situs inversus syndrome
  • Atrial situs inversus
  • Complete situs inversus with dextrocardia
  • Congenital malposition of heart
  • Congenital malposition of heart
  • Dextrocardia
  • Dextrocardia
  • Dextrocardia/situs inversus finding
  • Immotile cilia syndrome
  • Kartagener syndrome
  • Laterality sequence
  • Situs inversus abdominalis
  • Situs inversus thoracis
  • Situs inversus viscerum
  • Situs inversus with levocardia

Diagnostic Related Group(s)

The code Q89.3 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Other Digestive System Diagnoses With Mcc (393)
  • Other Digestive System Diagnoses With Cc (394)
  • Other Digestive System Diagnoses Without Cc/mcc (395)

References to Index of Diseases and Injuries

The code Q89.3 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Dextrocardia with situs inversus
    • Mirror-image atrial arrangement with situs inversus
    • Situs inversus or transversus abdominalis
    • Situs inversus or transversus thoracis
    • Transposition of abdominal viscera
    • Transposition of thoracic viscera
  • Type 1 Excludes Notes:
    • dextrocardia NOS (@Q24.0*)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q89.3 Right Arrow 759.3 Situs inversus

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q89 Other congenital malformations, not elsewhere classified
Q89.0 Congenital absence and malformations of spleen
Q89.01 Asplenia (congenital)
Q89.09 Congenital malformations of spleen
Q89.1 Congenital malformations of adrenal gland
Q89.2 Congenital malformations of other endocrine glands
Q89.4 Conjoined twins
Q89.7 Multiple congenital malformations, not elsewhere classified
Q89.8 Other specified congenital malformations
Q89.9 Congenital malformation, unspecified


This page was last updated on: 10/1/2023