270.0 AMINO-ACID TRANSPORT DIS


Code Information

Diagnosis Code: 270.0

Short Description: Amino-acid transport dis

Long Description: Disturbances of amino-acid transport

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 270 Disorders of amino-acid transport and metabolism
        • 270.0 Amino-acid transport dis

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 270.0 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Abderhalden-Kaufmann-Lignac syndrome (cystinosis) 270.0
  • Beta-mercaptolactate-cysteine disulfiduria 270.0
  • Blue
    • diaper syndrome 270.0
  • Cystinosis (malignant) 270.0
  • Cystinuria 270.0
  • Deficiency, deficient
    • sulfite oxidase 270.0
  • Deposit
    • cornea, corneal NEC 371.10
      • in
        • cystinosis 270.0 [371.15]
  • de Toni-Fanconi syndrome (cystinosis) 270.0
  • Diathesis
    • cystine (familial) 270.0
  • Disease, diseased - see also Syndrome
    • cystine storage (with renal sclerosis) 270.0
    • H 270.0
    • Hart's (pellagra-cerebellar ataxia-renal aminoaciduria) 270.0
    • Hartnup (pellagra-cerebellar ataxia-renal aminoaciduria) 270.0
    • Lignac's (cystinosis) 270.0
  • Disorder - see also Disease
    • amino acid (metabolic) (see also Disturbance, metabolism, amino acid) 270.9
      • cystinosis 270.0
      • cystinuria 270.0
      • glycinuria 270.0
      • renal transport NEC 270.0
      • transport NEC 270.0
        • renal 270.0
    • metabolism NEC 277.9
      • cystine storage 270.0
      • cystinuria 270.0
  • Disturbance - see also Disease
    • amino acid (metabolic) (see also Disorder, amino acid) 270.9
      • transport 270.0
    • metabolism (acquired) (congenital) (see also Disorder, metabolism) 277.9
      • amino acid (see also Disorder, amino acid) 270.9
        • transport 270.0
  • Disulfiduria, beta-mercaptolactate-cysteine 270.0
  • Dwarf, dwarfism 259.4
    • nephrotic-glycosuric, with hypophosphatemic rickets 270.0
  • Fanconi (-de Toni) (-Debr�) syndrome (cystinosis) 270.0
  • Glycinuria (renal) (with ketosis) 270.0
  • Hart's disease or syndrome (pellagra-cerebellar ataxia-renal aminoaciduria) 270.0
  • Hartnup disease (pellagra-cerebellar ataxia-renal aminoaciduria) 270.0
  • H disease 270.0
  • Hyperaminoaciduria 270.9
    • cystine 270.0
    • glycine 270.0
    • renal (types I, II, III) 270.0
  • Lignac's disease (cystinosis) 270.0
  • Lignac (-de Toni) (-Fanconi) (-Debr�) syndrome (cystinosis) 270.0
  • Lignac (-Fanconi) syndrome (cystinosis) 270.0
  • Pellagra-cerebellar-ataxia-renal aminoaciduria syndrome 270.0
  • Rickets (active) (acute) (adolescent) (adult) (chest wall) (congenital) (current) (infantile) (intestinal) 268.0
    • hypophosphatemic with nephrotic-glycosuric dwarfism 270.0
  • Sclerosis, sclerotic
    • renal 587
      • with
        • cystine storage disease 270.0
  • Stone(s) - see also Calculus
    • cystine 270.0
  • Syndrome - see also Disease
    • blue
      • diaper 270.0
    • de Toni-Fanconi (-Debre) (cystinosis) 270.0
    • Fanconi (-de Toni) (-Debr�) (cystinosis) 270.0
    • Hart's (pellagra-cerebellar ataxia-renal aminoaciduria) 270.0
    • Lignac (-de Toni) (-Fanconi) (-Debr�) (cystinosis) 270.0
    • pellagra-cerebellar ataxia-renal aminoaciduria 270.0
    • Toni-Fanconi (cystinosis) 270.0
  • Thesaurismosis
    • cystine 270.0
  • Toni-Fanconi syndrome (cystinosis) 270.0

Crosswalk Information

The code 270.0 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
270.0 Right Arrow E72.00 Disorders of amino-acid transport, unspecified
E72.01 Cystinuria
E72.04 Cystinosis
E72.09 Other disorders of amino-acid transport
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
270.1 Phenylketonuria [PKU]
270.2 Other disturbances of aromatic amino-acid metabolism
270.3 Disturbances of branched-chain amino-acid metabolism
270.4 Disturbances of sulphur-bearing amino-acid metabolism
270.5 Disturbances of histidine metabolism
270.6 Disorders of urea cycle metabolism
270.7 Other disturbances of straight-chain amino-acid metabolism
270.8 Other specified disorders of amino-acid metabolism
270.9 Unspecified disorder of amino-acid metabolism


This page was last updated on: 10/1/2014