270.4 SULPH AMINO-ACID MET DIS


Code Information

Diagnosis Code: 270.4

Short Description: Sulph amino-acid met dis

Long Description: Disturbances of sulphur-bearing amino-acid metabolism

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 270 Disorders of amino-acid transport and metabolism
        • 270.4 Sulph amino-acid met dis

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 270.4 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Cystathioninemia 270.4
  • Cystathioninuria 270.4
  • Deficiency, deficient
    • methylenetetrahydrofolate reductase (MTHFR) 270.4
  • Disorder - see also Disease
    • amino acid (metabolic) (see also Disturbance, metabolism, amino acid) 270.9
      • cystathioninuria 270.4
      • homocystinuria 270.4
  • Disturbance - see also Disease
    • metabolism (acquired) (congenital) (see also Disorder, metabolism) 277.9
      • amino acid (see also Disorder, amino acid) 270.9
        • sulfur-bearing 270.4
      • cystathionine 270.4
      • homocystine 270.4
      • methionine 270.4
  • Homocystinemia 270.4
  • Homocystinuria 270.4
  • Hypermethioninemia 270.4
  • Malabsorption 579.9
    • methionine 270.4
  • Methioninemia 270.4

Crosswalk Information

The code 270.4 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
270.4 Right Arrow E72.10 Disorders of sulfur-bearing amino-acid metabolism, unsp
E72.11 Homocystinuria
E72.19 Other disorders of sulfur-bearing amino-acid metabolism
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
270.0 Disturbances of amino-acid transport
270.1 Phenylketonuria [PKU]
270.2 Other disturbances of aromatic amino-acid metabolism
270.3 Disturbances of branched-chain amino-acid metabolism
270.5 Disturbances of histidine metabolism
270.6 Disorders of urea cycle metabolism
270.7 Other disturbances of straight-chain amino-acid metabolism
270.8 Other specified disorders of amino-acid metabolism
270.9 Unspecified disorder of amino-acid metabolism


This page was last updated on: 10/1/2014