270.7 STRAIG AMIN-ACID MET NEC


Code Information

Diagnosis Code: 270.7

Short Description: Straig amin-acid met NEC

Long Description: Other disturbances of straight-chain amino-acid metabolism

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 270 Disorders of amino-acid transport and metabolism
        • 270.7 Straig amin-acid met NEC

Code Version: 2015 ICD-9-CM


Synonyms

  • 3-Phosphoglycerate dehydrogenase deficiency
  • Adenosylcobalamin and methylcobalamin synthesis defect
  • Complete deficiency of methylmalonyl-coenzyme A mutase
  • Disorder of glutamine metabolism
  • Disorder of glycine metabolism
  • Disorder of lysine and hydroxylysine metabolism
  • Disorder of lysine AND/OR hydroxylysine metabolism
  • Disorder of serine metabolism
  • Disorder of threonine metabolism
  • Glucoglycinuria
  • Glutaric aciduria, type 1
  • Glutaryl-coenzyme A dehydrogenase deficiency
  • Glycine dehydrogenase
  • Hyperglycinemia
  • Hyperlysinemia
  • Impaired fasting glycaemia
  • Lysine intolerance
  • Lysinuric protein intolerance, type 1
  • Lysinuric protein intolerance, type 2
  • Methylmalonic acidemia
  • Non-ketotic hyperglycinemia
  • Non-ketotic hyperglycinemia H protein deficiency
  • Non-ketotic hyperglycinemia L protein deficiency
  • Periodic hyperlysinemia
  • Periodic hyperlysinemia with hyperammonemia
  • Persistent hyperlysinemia
  • Pipecolic acidemia
  • Saccharopinuria
  • Transient neonatal hyperglycinemia

References to Index of Diseases and Injuries

The code 270.7 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Acidemia 276.2
    • pipecolic 270.7
  • Aciduria 791.9
    • glutaric
      • type I 270.7
    • methylmalonic 270.3
      • with glycinemia 270.7
  • Disorder - see also Disease
    • metabolism NEC 277.9
      • glutamine 270.7
      • glycine 270.7
      • lysine 270.7
      • serine 270.7
      • threonine 270.7
  • Disturbance - see also Disease
    • metabolism (acquired) (congenital) (see also Disorder, metabolism) 277.9
      • amino acid (see also Disorder, amino acid) 270.9
        • straight-chain NEC 270.7
      • glutamine 270.7
      • glycine 270.7
      • lysine 270.7
      • serine 270.7
      • threonine 270.7
  • Glucoglycinuria 270.7
  • Glycinemia (with methylmalonic acidemia) 270.7
  • Hyperaminoaciduria 270.9
    • lysine 270.7
  • Hyperglycinemia 270.7
  • Hyperlysinemia 270.7
  • Hyperpipecolatemia 270.7
  • Intolerance
    • lysine (congenital) 270.7
    • protein (familial) 270.7
  • Saccharopinuria 270.7

Crosswalk Information

The code 270.7 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
270.7 Right Arrow E72.3 Disorders of lysine and hydroxylysine metabolism
E72.8 Other specified disorders of amino-acid metabolism
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
270.0 Disturbances of amino-acid transport
270.1 Phenylketonuria [PKU]
270.2 Other disturbances of aromatic amino-acid metabolism
270.3 Disturbances of branched-chain amino-acid metabolism
270.4 Disturbances of sulphur-bearing amino-acid metabolism
270.5 Disturbances of histidine metabolism
270.6 Disorders of urea cycle metabolism
270.8 Other specified disorders of amino-acid metabolism
270.9 Unspecified disorder of amino-acid metabolism


This page was last updated on: 10/1/2014