270.9 DIS AMINO-ACID METAB NOS


Code Information

Diagnosis Code: 270.9

Short Description: Dis amino-acid metab NOS

Long Description: Unspecified disorder of amino-acid metabolism

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 270 Disorders of amino-acid transport and metabolism
        • 270.9 Dis amino-acid metab NOS

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 270.9 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Acid
    • deficiency
      • amino 270.9
  • Aciduria 791.9
    • organic 270.9
  • Amino acid
    • deficiency 270.9
      • anemia 281.4
    • metabolic disorder (see also Disorder, amino acid) 270.9
  • Aminoaciduria 270.9
    • imidazole 270.5
  • Deficiency, deficient
    • amino acid 270.9
  • Disorder - see also Disease
    • amino acid (metabolic) (see also Disturbance, metabolism, amino acid) 270.9
      • albinism 270.2
      • alkaptonuria 270.2
      • argininosuccinicaciduria 270.6
      • beta-amino-isobutyricaciduria 277.2
      • cystathioninuria 270.4
      • cystinosis 270.0
      • cystinuria 270.0
      • glycinuria 270.0
      • homocystinuria 270.4
      • imidazole 270.5
      • maple syrup (urine) disease 270.3
      • neonatal, transitory 775.89
      • oasthouse urine disease 270.2
      • ochronosis 270.2
      • phenylketonuria 270.1
      • phenylpyruvic oligophrenia 270.1
      • purine NEC 277.2
      • pyrimidine NEC 277.2
      • renal transport NEC 270.0
      • specified type NEC 270.8
      • transport NEC 270.0
        • renal 270.0
      • xanthinuria 277.2
    • metabolism NEC 277.9
      • amino acid (see also Disorder, amino acid) 270.9
        • specified type NEC 270.8
      • nitrogen 270.9
  • Disturbance - see also Disease
    • amino acid (metabolic) (see also Disorder, amino acid) 270.9
      • imidazole 270.5
      • maple syrup (urine) disease 270.3
      • transport 270.0
    • metabolism (acquired) (congenital) (see also Disorder, metabolism) 277.9
      • amino acid (see also Disorder, amino acid) 270.9
        • aromatic NEC 270.2
        • branched-chain 270.3
        • specified type NEC 270.8
        • straight-chain NEC 270.7
        • sulfur-bearing 270.4
        • transport 270.0
  • Hyperaminoaciduria 270.9
    • arginine 270.6
    • citrulline 270.6
    • cystine 270.0
    • glycine 270.0
    • lysine 270.7
    • ornithine 270.6
    • renal (types I, II, III) 270.0

Crosswalk Information

The code 270.9 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
270.9 Right Arrow E72.9 Disorder of amino-acid metabolism, unspecified
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
270.0 Disturbances of amino-acid transport
270.1 Phenylketonuria [PKU]
270.2 Other disturbances of aromatic amino-acid metabolism
270.3 Disturbances of branched-chain amino-acid metabolism
270.4 Disturbances of sulphur-bearing amino-acid metabolism
270.5 Disturbances of histidine metabolism
270.6 Disorders of urea cycle metabolism
270.7 Other disturbances of straight-chain amino-acid metabolism
270.8 Other specified disorders of amino-acid metabolism


This page was last updated on: 10/1/2014