272.7 LIPIDOSES


Code Information

Diagnosis Code: 272.7

Short Description: Lipidoses

Long Description: Lipidoses

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 272 Disorders of lipoid metabolism
        • 272.7 Lipidoses

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 272.7 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Anderson's disease 272.7
  • Anemia 285.9
    • splenic 285.8
      • familial (Gaucher's) 272.7
  • Angiokeratoma (M9141/0) - see also Neoplasm, skin, benign
    • corporis diffusum 272.7
  • Angiokeratosis
    • diffuse 272.7
  • Angiomatosis 757.32
    • corporis diffusum universale 272.7
  • Cerebrosidosis 272.7
  • Ceroid storage disease 272.7
  • Degeneration, degenerative
    • brain (cortical) (progressive) 331.9
      • in
        • Babry's disease 272.7 [330.2]
        • Gaucher's disease 272.7 [330.2]
        • lipidosis
          • generalized 272.7 [330.2]
        • Niemann-Pick disease 272.7 [330.2]
        • sphingolipidosis 272.7 [330.2]
  • Diabetes, diabetic (brittle) (congenital) (familial) (mellitus) (severe) (slight) (without complication) 250.0
    • lipoidosis 250.8 [272.7]
      • due to secondary diabetes 249.8 [272.7]
    • secondary (chemical-induced) (due to chronic condition) (due to infection) (drug-induced) 249.0
      • lipoidosis 249.8 [272.7]
  • Disease, diseased - see also Syndrome
    • Anderson's (angiokeratoma corporis diffusum) 272.7
    • ceroid storage 272.7
    • Fabry's (angiokeratoma corporis diffusum) 272.7
    • Gaucher's (adult) (cerebroside lipidosis) (infantile) 272.7
    • I cell 272.7
    • lipidosis 272.7
    • lipoid storage NEC 272.7
    • mucolipidosis (I) (II) (III) 272.7
    • Niemann-Pick (lipid histiocytosis) 272.7
    • Pick's
      • lipid histiocytosis 272.7
    • pseudo-Hurler's (mucolipidosis III) 272.7
    • storage
      • lipid 272.7
    • Sweeley-Klionsky 272.7
    • triglyceride-storage, type I, II, III 272.7
    • Wolman's (primary familial xanthomatosis) 272.7
  • Disorder - see also Disease
    • lipid
      • storage 272.7
    • metabolism NEC 277.9
      • lipid 272.9
        • storage 272.7
  • Disturbance - see also Disease
    • metabolism (acquired) (congenital) (see also Disorder, metabolism) 277.9
      • phosphatides 272.7
  • Dystrophy, dystrophia 783.9
    • retina, retinal (hereditary) 362.70
      • in
        • systemic lipidosis 272.7 [362.71]
  • Fabry's disease (angiokeratoma corporis diffusum) 272.7
  • Gaucher's
    • disease (adult) (cerebroside lipidosis) (infantile) 272.7
    • hepatomegaly 272.7
    • splenomegaly (cerebroside lipidosis) 272.7
  • Hepatomegaly (see also Hypertrophy, liver) 789.1
    • Gaucher's 272.7
  • Histiocytosis (acute) (chronic) (subacute) 277.89
    • lipid, lipoid (essential) 272.7
  • Hyperlipidosis 272.7
    • hereditary 272.7
  • Lipidosis 272.7
    • cephalin 272.7
    • cerebral (infantile) (juvenile) (late) 330.1
    • cerebroretinal 330.1 [362.71]
    • cerebroside 272.7
    • cerebrospinal 272.7
    • chemically-induced 272.7
    • cholesterol 272.7
    • diabetic 250.8 [272.7]
      • due to secondary diabetes 249.8 [272.7]
    • dystopic (hereditary) 272.7
    • glycolipid 272.7
    • hepatosplenomegalic 272.3
    • hereditary, dystopic 272.7
    • sulfatide 330.0
  • Lipoid - see also condition
    • histiocytosis 272.7
      • essential 272.7
  • Lipoidosis (see also Lipidosis) 272.7
  • Mucolipidosis I, II, III 272.7
  • Niemann-Pick disease (lipid histiocytosis) (splenomegaly) 272.7
  • Pick's
    • disease
      • lipid histiocytosis 272.7
  • Pick-Niemann disease (lipid histiocytosis) 272.7
  • Pseudo-Hurler's disease (mucolipidosis III) 272.7
  • Purpura 287.2
    • hemorrhagic (see also Purpura, thrombocytopenic) 287.39
      • nodular 272.7
  • Ruiter-Pompen (-Wyers) syndrome (angiokeratoma corporis diffusum) 272.7
  • Sea-blue histiocyte syndrome 272.7
  • Sphingolipidosis 272.7
  • Sphingolipodystrophy 272.7
  • Sphingomyelinosis 272.7
  • Splenomegaly 789.2
    • Gaucher's (cerebroside lipidosis) 272.7
    • Niemann-Pick (lipid histiocytosis) 272.7
  • Sweeley-Klionsky disease (angiokeratoma corporis diffusum) 272.7
  • Syndrome - see also Disease
    • cardiovasorenal 272.7
    • Fabry (-Anderson) (angiokeratoma corporis diffusum) 272.7
    • Niemann-Pick (lipid histiocytosis) 272.7
    • Ruiter-Pompen (-Wyers) (angiokeratoma corporis diffusum) 272.7
    • sea-blue histiocyte 272.7
  • Thesaurismosis
    • kerasin 272.7
    • lipoid 272.7
    • phosphatide 272.7
  • Trihexosidosis 272.7
  • Wolman's disease (primary familial xanthomatosis) 272.7
  • Xanthoma(s), xanthomatosis 272.2
    • bone 272.7
    • cutaneotendinous 272.7
    • disseminatum 272.7
    • familial 272.7
    • hereditary 272.7
    • infantile 272.7
    • joint 272.7
    • juvenile 272.7
    • multiple 272.7
    • multiplex 272.7
    • primary familial 272.7
    • tendon (sheath) 272.7

Crosswalk Information

The code 272.7 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
272.7 Right Arrow E75.21 Fabry (-Anderson) disease
E75.22 Gaucher disease
E75.249 Niemann-Pick disease, unspecified
E77.0 Defects in post-translational mod of lysosomal enzymes
E77.1 Defects in glycoprotein degradation
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
272.0 Pure hypercholesterolemia
272.1 Pure hyperglyceridemia
272.2 Mixed hyperlipidemia
272.3 Hyperchylomicronemia
272.4 Other and unspecified hyperlipidemia
272.5 Lipoprotein deficiencies
272.6 Lipodystrophy
272.8 Other disorders of lipoid metabolism
272.9 Unspecified disorder of lipoid metabolism


This page was last updated on: 10/1/2014