275.01 HEREDIT HEMOCHROMATOSIS


Code Information

Diagnosis Code: 275.01

Short Description: Heredit hemochromatosis

Long Description: Hereditary hemochromatosis

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 275 Disorders of mineral metabolism
        • 275.01 Heredit hemochromatosis

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 275.01 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Bronze, bronzed
    • diabetes 275.01
  • Cirrhosis, cirrhotic 571.5
    • due to
      • bronzed diabetes 275.01
    • liver (chronic) (hepatolienal) (hypertrophic) (nodular) (splenomegalic) (unilobar) 571.5
      • pigmentary 275.01
    • pigment, pigmentary (of liver) 275.01
  • Diabetes, diabetic (brittle) (congenital) (familial) (mellitus) (severe) (slight) (without complication) 250.0
    • bronze, bronzed 275.01
  • Hanot-Chauffard (-Troisier) syndrome (bronze diabetes) 275.01
  • Hemochromatosis (acquired) (liver) (myocardium) (secondary) 275.03
    • hereditary 275.01
    • primary idiopathic 275.01
  • Syndrome - see also Disease
    • Hanot-Chauffard (-Troisier) (bronze diabetes) 275.01
    • Troisier-Hanot-Chauffard (bronze diabetes) 275.01
  • Troisier-Hanot-Chauffard syndrome (bronze diabetes) 275.01

Crosswalk Information

The code 275.01 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
275.01 Right Arrow E83.110 Hereditary hemochromatosis
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
275.02 Hemochromatosis due to repeated red blood cell transfusions
275.03 Other hemochromatosis
275.09 Other disorders of iron metabolism
275.1 Disorders of copper metabolism
275.2 Disorders of magnesium metabolism
275.3 Disorders of phosphorus metabolism
275.40 Unspecified disorder of calcium metabolism
275.41 Hypocalcemia
275.42 Hypercalcemia
275.49 Other disorders of calcium metabolism
275.5 Hungry bone syndrome
275.8 Other specified disorders of mineral metabolism
275.9 Unspecified disorder of mineral metabolism


This page was last updated on: 10/1/2014