277.00 CYSTIC FIBROS W/O ILEUS


Code Information

Diagnosis Code: 277.00

Short Description: Cystic fibros w/o ileus

Long Description: Cystic fibrosis without mention of meconium ileus

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 277 Other and unspecified disorders of metabolism
        • 277.00 Cystic fibros w/o ileus

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 277.00 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Cirrhosis, cirrhotic 571.5
    • due to
      • cystic fibrosis 277.00
  • Cystic - see also condition
    • fibrosis (pancreas) 277.00
      • with
        • manifestations
          • gastrointestinal 277.03
          • pulmonary 277.02
          • specified NEC 277.09
        • meconium ileus 277.01
        • pulmonary exacerbation 277.02
  • Disease, diseased - see also Syndrome
    • pancreas 577.9
      • fibrocystic 277.00
  • Fibrocystic
    • disease 277.00
      • bone NEC 733.29
      • breast 610.1
      • jaw 526.2
      • kidney (congenital) 753.19
      • liver 751.62
      • lung 518.89
        • congenital 748.4
      • pancreas 277.00
  • Fibrosis, fibrotic
    • cystic (of pancreas) 277.00
      • with
        • manifestations
          • gastrointestinal 277.03
          • pulmonary 277.02
          • specified NEC 277.09
        • meconium ileus 277.01
        • pulmonary exacerbation 277.02
    • pancreas 577.8
      • cystic 277.00
        • with
          • manifestations
            • gastrointestinal 277.03
            • pulmonary 277.02
            • specified NEC 277.09
          • meconium ileus 277.01
          • pulmonary exacerbation 277.02
  • Hyperviscidosis 277.00
  • Mucoviscidosis 277.00
    • with meconium obstruction 277.01

Crosswalk Information

The code 277.00 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
277.00 Right Arrow E84.9 Cystic fibrosis, unspecified
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
277.01 Cystic fibrosis with meconium ileus
277.02 Cystic fibrosis with pulmonary manifestations
277.03 Cystic fibrosis with gastrointestinal manifestations
277.09 Cystic fibrosis with other manifestations
277.1 Disorders of porphyrin metabolism
277.2 Other disorders of purine and pyrimidine metabolism
277.30 Amyloidosis, unspecified
277.31 Familial Mediterranean fever
277.39 Other amyloidosis
277.4 Disorders of bilirubin excretion
277.5 Mucopolysaccharidosis
277.6 Other deficiencies of circulating enzymes
277.7 Dysmetabolic syndrome X
277.81 Primary carnitine deficiency
277.82 Carnitine deficiency due to inborn errors of metabolism
277.83 Iatrogenic carnitine deficiency
277.84 Other secondary carnitine deficiency
277.85 Disorders of fatty acid oxidation
277.86 Peroxisomal disorders
277.87 Disorders of mitochondrial metabolism
277.88 Tumor lysis syndrome
277.89 Other specified disorders of metabolism
277.9 Unspecified disorder of metabolism


This page was last updated on: 10/1/2014