277.31 FAM MEDITERRANEAN FEVER


Code Information

Diagnosis Code: 277.31

Short Description: Fam Mediterranean fever

Long Description: Familial Mediterranean fever

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 277 Other and unspecified disorders of metabolism
        • 277.31 Fam Mediterranean fever

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 277.31 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Abdominalgia 789.0
    • periodic 277.31
  • Armenian disease 277.31
  • Arthritis, arthritic (acute) (chronic) (subacute) 716.9
    • due to or associated with
      • Mediterranean fever, familial 277.31 [713.7]
  • Disease, diseased - see also Syndrome
    • Armenian 277.31
    • familial periodic 277.31
      • paralysis 359.3
    • periodic (familial) (Reimann's) NEC 277.31
      • paralysis 359.3
    • Reimann's (periodic) 277.31
    • Siegal-Cattan-Mamou (periodic) 277.31
  • Fever 780.60
    • etiocholanolone 277.31
    • Mediterranean (see also Brucellosis) 023.9
      • familial 277.31
    • periodic 277.31
  • Mediterranean
    • fever (see also Brucellosis) 023.9
      • familial 277.31
  • Nephropathy (see also Nephritis) 583.9
    • hereditary amyloid 277.31
  • Periodic - see also condition
    • disease (familial) 277.31
    • fever 277.31
    • peritonitis 277.31
    • polyserositis 277.31
  • Peritonitis (acute) (adhesive) (fibrinous) (hemorrhagic) (idiopathic) (localized) (perforative) (primary) (with adhesions) (with effusion) 567.9
    • paroxysmal, benign 277.31
    • periodic (familial) 277.31
  • Polyserositis (peritoneal) 568.82
    • paroxysmal (familial) 277.31
    • periodic (familial) 277.31
    • recurrent 277.31
  • Reimann's periodic disease 277.31
  • Siegal-Cattan-Mamou disease (periodic) 277.31
  • Syndrome - see also Disease
    • Armenian 277.31
    • periodic 277.31

Crosswalk Information

The code 277.31 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
277.31 Right Arrow E85.0 Non-neuropathic heredofamilial amyloidosis
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
277.00 Cystic fibrosis without mention of meconium ileus
277.01 Cystic fibrosis with meconium ileus
277.02 Cystic fibrosis with pulmonary manifestations
277.03 Cystic fibrosis with gastrointestinal manifestations
277.09 Cystic fibrosis with other manifestations
277.1 Disorders of porphyrin metabolism
277.2 Other disorders of purine and pyrimidine metabolism
277.30 Amyloidosis, unspecified
277.39 Other amyloidosis
277.4 Disorders of bilirubin excretion
277.5 Mucopolysaccharidosis
277.6 Other deficiencies of circulating enzymes
277.7 Dysmetabolic syndrome X
277.81 Primary carnitine deficiency
277.82 Carnitine deficiency due to inborn errors of metabolism
277.83 Iatrogenic carnitine deficiency
277.84 Other secondary carnitine deficiency
277.85 Disorders of fatty acid oxidation
277.86 Peroxisomal disorders
277.87 Disorders of mitochondrial metabolism
277.88 Tumor lysis syndrome
277.89 Other specified disorders of metabolism
277.9 Unspecified disorder of metabolism


This page was last updated on: 10/1/2014