277.85 DISORDERS ACID OXIDATION


Code Information

Diagnosis Code: 277.85

Short Description: Disorders acid oxidation

Long Description: Disorders of fatty acid oxidation

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 277 Other and unspecified disorders of metabolism
        • 277.85 Disorders acid oxidation

Code Version: 2015 ICD-9-CM


Synonyms

  • 2-methylbutyrylglycinuria
  • Acyl-coenzyme A dehydrogenase deficiency
  • Carnitine palmitoyltransferase deficiency
  • Carnitine palmitoyltransferase I deficiency
  • Carnitine palmitoyltransferase II deficiency
  • Deficiency of butyryl-CoA dehydrogenase
  • Glutaric aciduria, type 2
  • Long chain acyl-coenzyme A dehydrogenase deficiency
  • Long-chain fatty acid transport deficiency
  • Medium-chain acyl-coenzyme A dehydrogenase deficiency
  • Mitochondrial trifunctional protein deficiency
  • Very long chain acyl-coenzyme A dehydrogenase deficiency

References to Index of Diseases and Injuries

The code 277.85 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Aciduria 791.9
    • glutaric
      • type II (type IIA, IIB, IIC) 277.85
  • Deficiency, deficient
    • carnitine 277.81
      • palmitoyltransferase (CPT1, CPT2) 277.85
      • palmityl transferase (CPT1, CPT2) 277.85
    • long chain 3-hydroxyacyl CoA dehydrogenase (LCHAD) 277.85
    • long chain/very long chain acyl CoA dehydrogenase (LCAD, VLCAD) 277.85
    • medium chain acyl CoA dehydrogenase (MCAD) 277.85
    • short chain acyl CoA dehydrogenase (SCAD) 277.85
  • Disorder - see also Disease
    • fatty acid oxidation 277.85
    • metabolism NEC 277.9
      • fatty acid oxidation 277.85
    • oxidation, fatty acid 277.85
  • LCAD (long chain/very long chain acyl CoA dehydrogenase deficiency, VLCAD) 277.85
  • LCHAD (long chain 3-hydroxyacyl CoA dehydrogenase deficiency) 277.85
  • MCAD (medium chain acyl CoA dehydrogenase deficiency) 277.85
  • Short, shortening, shortness
    • chain acyl CoA dehydrogenase deficiency (SCAD) 277.85
  • VLCAD (long chain/very long chain acyl CoA dehydrogenase deficiency, LCAD) 277.85

Crosswalk Information

The code 277.85 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
277.85 Right Arrow E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency
E71.311 Medium chain acyl CoA dehydrogenase deficiency
E71.312 Short chain acyl CoA dehydrogenase deficiency
E71.313 Glutaric aciduria type II
E71.314 Muscle carnitine palmitoyltransferase deficiency
E71.318 Other disorders of fatty-acid oxidation
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
277.00 Cystic fibrosis without mention of meconium ileus
277.01 Cystic fibrosis with meconium ileus
277.02 Cystic fibrosis with pulmonary manifestations
277.03 Cystic fibrosis with gastrointestinal manifestations
277.09 Cystic fibrosis with other manifestations
277.1 Disorders of porphyrin metabolism
277.2 Other disorders of purine and pyrimidine metabolism
277.30 Amyloidosis, unspecified
277.31 Familial Mediterranean fever
277.39 Other amyloidosis
277.4 Disorders of bilirubin excretion
277.5 Mucopolysaccharidosis
277.6 Other deficiencies of circulating enzymes
277.7 Dysmetabolic syndrome X
277.81 Primary carnitine deficiency
277.82 Carnitine deficiency due to inborn errors of metabolism
277.83 Iatrogenic carnitine deficiency
277.84 Other secondary carnitine deficiency
277.86 Peroxisomal disorders
277.87 Disorders of mitochondrial metabolism
277.88 Tumor lysis syndrome
277.89 Other specified disorders of metabolism
277.9 Unspecified disorder of metabolism


This page was last updated on: 10/1/2014