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277.87 DIS MITOCHONDRIAL METAB


Code Information

Diagnosis Code: 277.87

Short Description: Dis mitochondrial metab

Long Description: Disorders of mitochondrial metabolism

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 277 Other and unspecified disorders of metabolism
        • 277.87 Dis mitochondrial metab

Code Version: 2015 ICD-9-CM


Synonyms

  • Juvenile myopathy, encephalopathy, lactic acidosis AND stroke
  • Kearns-Sayre syndrome
  • Mitochondrial encephalomyopathy
  • Myoclonus epilepsy AND ragged red fibers
  • Neurogenic muscle weakness, ataxia and retinitis pigmentosa
  • Pearson's syndrome

References to Index of Diseases and Injuries

The code 277.87 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Disorder - see also Disease
    • metabolism NEC 277.9
      • mitochondrial 277.87
    • mitochondrial metabolism 277.87
  • Fukuhara syndrome 277.87
  • Kearns-Sayre syndrome 277.87
  • MELAS syndrome (mitochondrial encephalopathy, lactic acidosis and stroke-like episodes)� 277.87
  • MERRF syndrome (myoclonus with epilepsy and with ragged red fibers) 277.87
  • Mitochondrial encephalopathy, lactic acidosis and stroke-like episodes (MELAS syndrome) 277.87
  • Mitochondrial neurogastrointestinal encephalopathy syndrome (MNGIE) 277.87
  • Myoclonus (familial essential) (multifocal) (simplex) 333.2
    • with epilepsy and with ragged red fibers� (MERRF syndrome) 277.87
  • NARP� (ataxia and retinitis pigmentosa syndrome) 277.87
  • Neuropathy, neuropathic (see also Disorder, nerve) 355.9
    • ataxia and retinitis pigmentosa� (NARP syndrome) 277.87
  • Syndrome - see also Disease
    • Fukuhara 277.87
    • Kearns-Sayre 277.87
    • MELAS (mitochondrial encephalopathy, lactic acidosis and stroke-like episodes)� 277.87
    • MERRF (myoclonus with epilepsy and with ragged red fibers) 277.87
    • mitochondrial neurogastrointestinal encephalopathy (MNGIE) 277.87
    • MNGIE (mitochondrial neurogastrointestinal encephalopathy) 277.87
    • NARP (neuropathy, ataxia and retinitis pigmentosa) 277.87

Crosswalk Information

The code 277.87 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
277.87 Right Arrow E88.40 Mitochondrial metabolism disorder, unspecified
E88.41 MELAS syndrome
E88.42 MERRF syndrome
E88.49 Other mitochondrial metabolism disorders
H49.819 Kearns-Sayre syndrome, unspecified eye
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
277.00 Cystic fibrosis without mention of meconium ileus
277.01 Cystic fibrosis with meconium ileus
277.02 Cystic fibrosis with pulmonary manifestations
277.03 Cystic fibrosis with gastrointestinal manifestations
277.09 Cystic fibrosis with other manifestations
277.1 Disorders of porphyrin metabolism
277.2 Other disorders of purine and pyrimidine metabolism
277.30 Amyloidosis, unspecified
277.31 Familial Mediterranean fever
277.39 Other amyloidosis
277.4 Disorders of bilirubin excretion
277.5 Mucopolysaccharidosis
277.6 Other deficiencies of circulating enzymes
277.7 Dysmetabolic syndrome X
277.81 Primary carnitine deficiency
277.82 Carnitine deficiency due to inborn errors of metabolism
277.83 Iatrogenic carnitine deficiency
277.84 Other secondary carnitine deficiency
277.85 Disorders of fatty acid oxidation
277.86 Peroxisomal disorders
277.88 Tumor lysis syndrome
277.89 Other specified disorders of metabolism
277.9 Unspecified disorder of metabolism

This page was last updated on: 10/1/2014

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