277.89 METABOLISM DISORDER NEC


Code Information

Diagnosis Code: 277.89

Short Description: Metabolism disorder NEC

Long Description: Other specified disorders of metabolism

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 277 Other and unspecified disorders of metabolism
        • 277.89 Metabolism disorder NEC

Code Version: 2015 ICD-9-CM


Synonyms

  • Acatalasemia
  • Acatalasia
  • Adenosine deaminase overproduction
  • Alpha-N-acetylgalactosaminidase deficiency
  • Anemia due to disorders of nucleotide metabolism
  • Angioedema due to disorder of kinin metabolism
  • Autosomal variant form of transthyretin
  • Combined complex deficiencies
  • Combined deficiency of long chain 3-hydroxyacyl-coenzyme A dehydrogenase and enoyl-coenzyme A hydratase
  • Defect in post-translational modification of lysosomal enzymes
  • Defective biosynthesis
  • Defective osmoregulation
  • Deficiency in enzyme complexes of mitochondrial respiratory chain
  • Deficiency of amylopectin 6-glucanohydrolase
  • Deficiency of glycosidase
  • Deficiency of halogenase
  • Deficiency of isobutyryl-coenzyme A dehydrogenase
  • Deficiency of limit dextrinase
  • Deficiency of protease
  • Deletion and duplication of mitochondrial deoxyribonucleic acid
  • Depletion of mitochondrial deoxyribonucleic acid
  • Disorder of beta alanine, carnosine AND/OR homocarnosine metabolism
  • Disorder of chromium metabolism
  • Disorder of glucose regulation
  • Disorder of glycoprotein metabolism
  • Disorder of glycosaminoglycan metabolism
  • Disorder of iodine metabolism
  • Disorder of mitochondrial respiratory chain complexes
  • Disorder of organic acid metabolism
  • Disorder of osmoregulation
  • Disorder of oxygen transport
  • Disorder of peroxisomal function
  • Disorder of protein metabolism
  • Disorder of pyruvate metabolism and mitochondrial respiratory chain
  • Disorder of sialic acid metabolism
  • Disorder of steroid metabolism
  • Disorder of strontium metabolism
  • Disorder with defective osteoid mineralization
  • Disorders of pyruvate metabolism and gluconeogenesis
  • Drug resistance to insulin
  • Enterokinase deficiency
  • Eosinophilic granuloma of bone
  • Extensive metabolizer due to cytochrome p450 CYP2D6 variant
  • Familial sea-blue histiocytosis
  • Fast acetylator due to N-acetyltransferase enzyme variant
  • Fat overload syndrome
  • Glutaric aciduria, type 1
  • Glutathione S-transferase deficiency
  • Hand-Schüller-Christian disease
  • Histiocytosis X syndrome
  • Homocarnosinase deficiency
  • Hyper-beta-carnosinemia
  • Hyperimidodipeptiduria due to proline dipeptidase deficiency
  • Hypermanganesemia with dystonia, polycythemia, and cirrhosis
  • Impaired oxygen extraction
  • Inborn error of pyruvate metabolism
  • Increased auto-oxidation
  • Increased fluid pressure
  • Increased oxygen demand
  • Inherited metabolic disorder of nervous system
  • Intermediate metabolizer due to cytochrome p450 CYP2D6 variant
  • Langerhans cell histiocytosis
  • Langerhans cell histiocytosis - Hashimoto-Pritzker type
  • Langerhans cell histiocytosis of lung
  • Langerhans cell histiocytosis, unifocal
  • Macroamylasemia
  • Methylene tetrahydrofolate methyltransferase reductase deficiency AND homocystinuria
  • Mucinous histiocytosis of the colon
  • Pancreatic colipase deficiency
  • Pancreatic triacylglycerol lipase deficiency
  • Phosphoenolpyruvate carboxykinase deficiency
  • Polyostotic sclerosing histiocytosis
  • Poor metabolizer due to cytochrome p450 CYP2C19 variant
  • Poor metabolizer due to cytochrome p450 CYP2C9 variant
  • Poor metabolizer due to cytochrome p450 CYP2D6 variant
  • Pseudoinfantile Refsum's disease
  • Pyruvate carboxylase deficiency
  • Pyruvate dehydrogenase complex deficiency
  • Refeeding syndrome
  • Sepiapterin reductase deficiency
  • Sinus histiocytosis with massive lymphadenopathy
  • Slow acetylator due to N-acetyltransferase enzyme variant
  • Solitary reticulohistiocytoma
  • Tetrahydrobiopterin synthesis defect
  • Trypsinogen deficiency
  • Tumor lysis syndrome
  • UGT1A1*28 polymorphism
  • Ultrarapid metabolizer due to cytochrome p450 CYP2D6 variant
  • Undetermined cell histiocytosis

References to Index of Diseases and Injuries

The code 277.89 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Acatalasemia 277.89
  • Acatalasia 277.89
  • Christian's syndrome (chronic histiocytosis X) 277.89
  • Disease, diseased - see also Syndrome
    • Christian's (chronic histiocytosis X) 277.89
    • Erdheim-Chester (ECD) 277.89
    • Hand-Sch�ller-Christian (chronic histiocytosis X) 277.89
    • Sch�ller-Christian (chronic histiocytosis X) 277.89
  • Disorder - see also Disease
    • metabolism NEC 277.9
      • specified type NEC 277.89
  • ECD (Erdheim-Chester disease) 277.89
  • Eosinophilic - see also condition
    • granuloma (bone) 277.89
  • Erdheim-Chester disease (ECD) 277.89
  • Granuloma NEC 686.1
    • bone (see also Osteomyelitis) 730.1
      • eosinophilic 277.89
    • eosinophilic 277.89
      • bone 277.89
      • lung 277.89
      • oral mucosa 528.9
    • lipid 277.89
    • lipoid 277.89
    • lung (infectious) (see also Fibrosis, lung) 515
      • eosinophilic 277.89
    • reticulohistiocytic 277.89
  • Granulomatosis NEC 686.1
    • lipoid 277.89
  • Hand-Sch�ller-Christian disease or syndrome (chronic histiocytosis x) 277.89
  • Histiocytosis (acute) (chronic) (subacute) 277.89
    • acute differentiated progressive (M9722/3) 202.5
    • adult pulmonary Langerhans cell (PLCH) 516.5
    • cholesterol 277.89
    • essential 277.89
    • lipid, lipoid (essential) 272.7
    • lipochrome (familial) 288.1
    • malignant (M9720/3) 202.3
    • non-Langerhans cell 277.89
    • polyostotic sclerosing 277.89
    • X (chronic) 277.89
      • acute (progressive) (M9722/3) 202.5
  • Metabolism disorder 277.9
    • specified type NEC 277.89
  • Reticulohistiocytoma (giant cell) 277.89
  • Sch�ller-Christian disease or syndrome (chronic histiocytosis X) 277.89
  • Syndrome - see also Disease
    • Christian's (chronic histiocytosis X) 277.89
    • Erdheim-Chester 277.89
    • Hand-Sch�ller-Christian (chronic histiocytosis X) 277.89
    • Sch�ller-Christian (chronic histiocytosis X) 277.89
  • Xanthoma(s), xanthomatosis 272.2
    • craniohypophyseal 277.89

Crosswalk Information

The code 277.89 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
277.89 Right Arrow C96.5 Multifocal and unisystemic Langerhans-cell histiocytosis
C96.6 Unifocal Langerhans-cell histiocytosis
E71.39 Other disorders of fatty-acid metabolism
E80.3 Defects of catalase and peroxidase
E88.89 Other specified metabolic disorders
E88.9 Metabolic disorder, unspecified
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
277.00 Cystic fibrosis without mention of meconium ileus
277.01 Cystic fibrosis with meconium ileus
277.02 Cystic fibrosis with pulmonary manifestations
277.03 Cystic fibrosis with gastrointestinal manifestations
277.09 Cystic fibrosis with other manifestations
277.1 Disorders of porphyrin metabolism
277.2 Other disorders of purine and pyrimidine metabolism
277.30 Amyloidosis, unspecified
277.31 Familial Mediterranean fever
277.39 Other amyloidosis
277.4 Disorders of bilirubin excretion
277.5 Mucopolysaccharidosis
277.6 Other deficiencies of circulating enzymes
277.7 Dysmetabolic syndrome X
277.81 Primary carnitine deficiency
277.82 Carnitine deficiency due to inborn errors of metabolism
277.83 Iatrogenic carnitine deficiency
277.84 Other secondary carnitine deficiency
277.85 Disorders of fatty acid oxidation
277.86 Peroxisomal disorders
277.87 Disorders of mitochondrial metabolism
277.88 Tumor lysis syndrome
277.9 Unspecified disorder of metabolism


This page was last updated on: 10/1/2014