284.01 CONSTITUTION RBC APLASIA


Code Information

Diagnosis Code: 284.01

Short Description: Constitution RBC aplasia

Long Description: Constitutional red blood cell aplasia

Code Classification:

  • Diseases of the blood and blood-forming organs (280–289)
    • Diseases of the blood and blood-forming organs (280-289)
      • 284 Aplastic anemia
        • 284.01 Constitution RBC aplasia

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 284.01 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Absence (organ or part) (complete or partial)
    • erythropoiesis 284.9
      • congenital 284.01
    • red cell 284.9
      • congenital 284.01
      • hereditary 284.01
  • Anemia 285.9
    • aplastic 284.9
      • congenital 284.01
      • constitutional 284.01
      • red cell (acquired) (adult) (with thymoma) 284.81
        • congenital 284.01
        • pure 284.01
    • aregenerative 284.9
      • congenital 284.01
    • chronica congenita aregenerativa 284.01
    • congenital (following fetal blood loss) 776.5
      • aplastic 284.01
    • Diamond-Blackfan (congenital hypoplastic) 284.01
    • hypoplasia, red blood cells 284.81
      • congenital or familial 284.01
    • hypoplastic (idiopathic) 284.9
      • congenital 284.01
      • familial 284.01
    • Joseph-Diamond-Blackfan (congenital hypoplastic) 284.01
    • pure red cell 284.81
      • congenital 284.01
  • Aplasia - see also Agenesis
    • bone marrow (myeloid) 284.9
      • congenital 284.01
    • congenital (pure) red cell 284.01
    • erythrocyte 284.81
      • congenital 284.01
    • red cell (with thymoma) 284.81
      • congenital 284.01
      • hereditary 284.01
      • of infants 284.01
      • primary 284.01
      • pure 284.01
        • due to drugs 284.81
  • Blackfan-Diamond anemia or syndrome (congenital hypoplastic anemia) 284.01
  • Diamond-Blackfan anemia or syndrome (congenital hypoplastic anemia) 284.01
  • Erythroblastopenia (acquired) 284.89
    • congenital 284.01
  • Erythroblastophthisis 284.01
  • Hypoplasia, hypoplasis 759.89
    • erythroid, congenital 284.01
  • Josephs-Diamond-Blackfan anemia (congenital hypoplastic) 284.01
  • Kaznelson's syndrome (congenital hypoplastic anemia) 284.01
  • Lymphoepithelioma (M8082/3) - see Neoplasm, by site, malignant
  • Syndrome - see also Disease
    • Blackfan-Diamond (congenital hypoplastic anemia) 284.01
    • Diamond-Blackfan (congenital hypoplastic anemia) 284.01
    • Joseph-Diamond-Blackfan (congenital hypoplastic anemia) 284.01
    • Kaznelson's (congenital hypoplastic anemia) 284.01
    • retroviral seroconversion (acute) V08
    • Schwachman's - see Syndrome, Shwachman's
    • suprarenal cortical 255.3
    • Werlhof-Wichmann (see also Purpura, thrombocytopenic) 287.39

Crosswalk Information

The code 284.01 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
284.01 Right Arrow D61.01 Constitutional (pure) red blood cell aplasia
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
284.09 Other constitutional aplastic anemia
284.11 Antineoplastic chemotherapy induced pancytopenia
284.12 Other drug-induced pancytopenia
284.19 Other pancytopenia
284.2 Myelophthisis
284.81 Red cell aplasia (acquired)(adult)(with thymoma)
284.89 Other specified aplastic anemias
284.9 Aplastic anemia, unspecified


This page was last updated on: 10/1/2014