330.1 CEREBRAL LIPIDOSES


Code Information

Diagnosis Code: 330.1

Short Description: Cerebral lipidoses

Long Description: Cerebral lipidoses

Code Classification:

  • Diseases of the nervous system (320–359)
    • Hereditary and degenerative diseases of the central nervous system (330-337)
      • 330 Cerebral degenerations usually manifest in childhood
        • 330.1 Cerebral lipidoses

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 330.1 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Amaurotic familial idiocy (infantile) (juvenile) (late) 330.1
  • Batten's disease, retina 330.1 [362.71]
  • Batten-Mayou disease 330.1 [362.71]
  • Bielschowsky's disease 330.1
  • Bielschowsky-Jansky
    • amaurotic familial idiocy 330.1
    • disease 330.1
  • Cerebromacular degeneration 330.1
  • Degeneration, degenerative
    • brain (cortical) (progressive) 331.9
      • in
        • lipidosis
          • cerebral 330.1
    • cerebromacular 330.1
  • Dementia 294.20
    • due to or associated with condition(s) classified elsewhere
      • cerebral lipidoses
        • with behavioral disturbance 330.1 [294.11]
        • without behavioral disturbance 330.1 [294.10]
  • Disease, diseased - see also Syndrome
    • Batten's 330.1 [362.71]
    • Batten-Mayou (retina) 330.1 [362.71]
    • Bielschowsky (-Jansky) 330.1
    • Jansky-Bielschowsky 330.1
    • Kufs' 330.1
    • retina, retinal NEC 362.9
      • batten's or Batten-Mayou 330.1 [362.71]
    • Sachs (-Tay) 330.1
    • Sandhoff's 330.1
    • Spielmeyer-Stock 330.1
    • Spielmeyer-Vogt 330.1
    • Tay-Sachs 330.1
    • Vogt-Spielmeyer 330.1
  • Dystrophy, dystrophia 783.9
    • retina, retinal (hereditary) 362.70
      • in
        • cerebroretinal lipidosis 330.1 [362.71]
  • Gangliosidosis 330.1
  • Idiot, idiocy (congenital) 318.2
    • amaurotic (Bielschowsky) (-Jansky) (family) (infantile (late)) (juvenile (late)) (Vogt-Spielmeyer) 330.1
  • Jansky-Bielschowsky amaurotic familial idiocy 330.1
  • Kufs' disease 330.1
  • Lipidosis 272.7
    • cerebral (infantile) (juvenile) (late) 330.1
    • cerebroretinal 330.1 [362.71]
  • Sachs (-Tay) disease (amaurotic familial idiocy) 330.1
  • Sandhoff's disease 330.1
  • Spielmeyer-Stock disease 330.1
  • Spielmeyer-Vogt disease 330.1
  • Tay-Sachs
    • amaurotic familial idiocy 330.1
    • disease 330.1
  • Vogt-Spielmeyer disease (amaurotic familial idiocy) 330.1

Crosswalk Information

The code 330.1 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
330.1 Right Arrow E75.02 Tay-Sachs disease
E75.19 Other gangliosidosis
E75.4 Neuronal ceroid lipofuscinosis
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
330.0 Leukodystrophy
330.2 Cerebral degeneration in generalized lipidoses
330.3 Cerebral degeneration of childhood in other diseases classified elsewhere
330.8 Other specified cerebral degenerations in childhood
330.9 Unspecified cerebral degeneration in childhood


This page was last updated on: 10/1/2014