742.0 ENCEPHALOCELE


Code Information

Diagnosis Code: 742.0

Short Description: Encephalocele

Long Description: Encephalocele

Code Classification:

  • Congenital anomalies (740–759)
    • Congenital anomalies (740-759)
      • 742 Other congenital anomalies of nervous system
        • 742.0 Encephalocele

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 742.0 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Absence (organ or part) (complete or partial)
    • roof of orbit (congenital) 742.0
    • skull bone 756.0
      • with
        • encephalocele 742.0
  • Agenesis - see also Absence, by site, congenital
    • roof of orbit 742.0
    • skull (bone) 756.0
      • with
        • encephalocele 742.0
  • Anomaly, anomalous (congenital) (unspecified type) 759.9
    • bone NEC 756.9
      • skull 756.0
        • with
          • encephalocele 742.0
    • skull (bone) 756.0
      • with
        • encephalocele 742.0
    • specified type NEC
      • bone(s) 756.9
        • skull 756.0
          • with
            • encephalocele 742.0
      • skull (bone(s)) 756.0
        • with
          • encephalocele 742.0
  • Arnold-Chiari obstruction or syndrome (see also Spina bifida) 741.0
    • type III 742.0
  • Cephalocele 742.0
  • Chiari's
    • malformation
      • type III 742.0
  • Deformity 738.9
    • skull (acquired) 738.19
      • congenital 756.0
        • with
          • encephalocele 742.0
  • Distortion (congenital)
    • skull bone(s) 756.0
      • with
        • encephalocele 742.0
  • Encephalocele 742.0
    • orbit 376.81
  • Encephalocystocele 742.0
  • Encephalomeningocele 742.0
  • Encephalomyelocele 742.0
  • Exencephalus, exencephaly 742.0
  • Hernia, hernial (acquired) (recurrent) 553.9
    • brain 348.4
      • congenital 742.0
    • cerebral 348.4
      • congenital 742.0
      • endaural 742.0
  • Hydrencephalocele (congenital) 742.0
  • Hydrencephalomeningocele (congenital) 742.0
  • Hydroencephalocele (congenital) 742.0
  • Hydroencephalomeningocele (congenital) 742.0
  • Hydromeningocele (spinal) (see also Spina bifida) 741.9
    • cranial 742.0
  • Hypoplasia, hypoplasis 759.89
    • skull (bone) 756.0
      • with
        • encephalocele 742.0
  • Imperfect
    • closure (congenital)
      • roof of orbit 742.0
      • skull 756.0
        • with
          • encephalocele 742.0
  • Malformation (congenital) - see also Anomaly
    • Chiari
      • type III 742.0
  • Meningocele (congenital) (spinal) (see also Spina bifida) 741.9
    • cerebral 742.0
    • cranial 742.0
  • Meningoencephalocele 742.0
    • syphilitic 094.89
      • congenital 090.49
  • Sinus - see also Fistula
    • pericranii 742.0
  • Syndrome - see also Disease
    • Arnold-Chiari (see also Spina bifida) 741.0
      • type III 742.0

Crosswalk Information

The code 742.0 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
742.0 Right Arrow Q01.9 Encephalocele, unspecified
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
742.1 Microcephalus
742.2 Congenital reduction deformities of brain
742.3 Congenital hydrocephalus
742.4 Other specified congenital anomalies of brain
742.51 Diastematomyelia
742.53 Hydromyelia
742.59 Other specified congenital anomalies of spinal cord
742.8 Other specified congenital anomalies of nervous system
742.9 Unspecified congenital anomaly of brain, spinal cord, and nervous system


This page was last updated on: 10/1/2014