757.33 CONG SKIN PIGMENT ANOMAL


Code Information

Diagnosis Code: 757.33

Short Description: Cong skin pigment anomal

Long Description: Congenital pigmentary anomalies of skin

Code Classification:

  • Congenital anomalies (740–759)
    • Congenital anomalies (740-759)
      • 757 Congenital anomalies of the integument
        • 757.33 Cong skin pigment anomal

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 757.33 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Angioma (M9120/0) (see also Hemangioma, by site) 228.00
    • pigmentosum et atrophicum 757.33
  • Anomaly, anomalous (congenital) (unspecified type) 759.9
    • pigmentation 709.00
      • congenital 757.33
  • Asboe-Hansen's disease (incontinentia pigmenti) 757.33
  • Atrophoderma, atrophodermia 701.9
    • pigmentosum 757.33
  • Bloch-Siemens syndrome (incontinentia pigmenti) 757.33
  • Bloch-Stauffer dyshormonal dermatosis 757.33
  • Bloch-Sulzberger disease or syndrome (incontinentia pigmenti) (melanoblastosis) 757.33
  • Chloasma 709.09
    • eyelid 374.52
      • congenital 757.33
  • Dermatosis 709.9
    • pigmentary NEC 709.00
      • Siemens-Bloch 757.33
  • Disease, diseased - see also Syndrome
    • Asboe-Hansen's (incontinentia pigmenti) 757.33
    • Bloch-Sulzberger (incontinentia pigmenti) 757.33
    • Kaposi's 757.33
      • lichen ruber 697.8
        • acuminatus 696.4
        • moniliformis 697.8
    • xeroderma pigmentosum 757.33
    • mast cell 757.33
      • systemic (M9741/3) 202.6
    • Nettleship's (urticaria pigmentosa) 757.33
    • Thomson's (congenital poikiloderma) 757.33
  • Incontinentia pigmenti 757.33
  • Kaposi's
    • disease 757.33
      • lichen ruber 696.4
        • acuminatus 696.4
        • moniliformis 697.8
    • xeroderma pigmentosum 757.33
  • Lioderma essentialis (cum melanosis et telangiectasia) 757.33
  • Mast cell
    • disease 757.33
      • systemic (M9741/3) 202.6
  • Mastocytosis 757.33
    • malignant (M9741/3) 202.6
    • systemic (M9741/3) 202.6
  • Melanoblastosis
    • Block-Sulzberger 757.33
    • cutis linearis sive systematisata 757.33
  • Melanocytosis, neurocutaneous 757.33
  • Melanosis 709.09
    • corii degenerativa 757.33
    • lenticularis progressiva 757.33
  • Mongolian, mongolianism, mongolism, mongoloid 758.0
    • spot 757.33
  • Naegeli's
    • syndrome (incontinentia pigmenti) 757.33
  • Nettleship's disease (urticaria pigmentosa) 757.33
  • Nevus (M8720/0) - see also Neoplasm, skin, benign
    • comedonicus 757.33
    • pigmented (M8720/0)
      • systematicus 757.33
    • unius lateris 757.33
    • verrucous 757.33
  • Pigmentation (abnormal) 709.00
    • anomalies NEC 709.00
      • congenital 757.33
    • lids (congenital) 757.33
      • acquired 374.52
    • scrotum, congenital 757.33
  • Poikiloderma 709.09
    • congenital 757.33
  • Rothmund (-Thomson) syndrome 757.33
  • Spots, spotting
    • Mongolian (pigmented) 757.33
  • Syndrome - see also Disease
    • Block-Siemens (incontinentia pigmenti) 757.33
    • Bloch-Sulzberger (incontinentia pigmenti) 757.33
    • mastocytosis 757.33
    • Rothmund's (congenital poikiloderma) 757.33
    • telangiectasis-pigmentation-cataract 757.33
  • Thomson's disease (congenital poikiloderma) 757.33
  • Urticaria 708.9
    • pigmentosa 757.33
  • Xanthelasmoidea 757.33
  • Xeroderma (congenital) 757.39
    • pigmentosum 757.33

Crosswalk Information

The code 757.33 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
757.33 Right Arrow Q82.1 Xeroderma pigmentosum
Q82.2 Congenital cutaneous mastocytosis
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
757.0 Hereditary edema of legs
757.1 Ichthyosis congenita
757.2 Dermatoglyphic anomalies
757.31 Congenital ectodermal dysplasia
757.32 Vascular hamartomas
757.39 Other specified anomalies of skin
757.4 Specified anomalies of hair
757.5 Specified anomalies of nails
757.6 Specified congenital anomalies of breast
757.8 Other specified anomalies of the integument
757.9 Unspecified congenital anomaly of the integument


This page was last updated on: 10/1/2014