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Taxonomy Codes
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Certain disorders involving the immune mechanism (D80-D89)
Immunodeficiency with predominantly antibody defects (D80)
D80
- Immunodeficiency with predominantly antibody defects
D80.0
- Hereditary hypogammaglobulinemia
D80.1
- Nonfamilial hypogammaglobulinemia
D80.2
- Selective deficiency of immunoglobulin A [IgA]
D80.3
- Selective deficiency of immunoglobulin G [IgG] subclasses
D80.4
- Selective deficiency of immunoglobulin M [IgM]
D80.5
- Immunodeficiency with increased immunoglobulin M [IgM]
D80.6
- Antibody defic w near-norm immunoglob or w hyperimmunoglob
D80.7
- Transient hypogammaglobulinemia of infancy
D80.8
- Other immunodeficiencies with predominantly antibody defects
D80.9
- Immunodeficiency with predominantly antibody defects, unsp
Combined immunodeficiencies (D81)
D81
- Combined immunodeficiencies
D81.0
- Severe combined immunodeficiency with reticular dysgenesis
D81.1
- Severe combined immunodeficiency w low T- and B-cell numbers
D81.2
- Severe combined immunodef w low or normal B-cell numbers
D81.3
- Adenosine deaminase [ADA] deficiency
D81.30
- Adenosine deaminase deficiency, unspecified
D81.31
- Severe combined immunodef due to adenosine deaminase defic
D81.32
- Adenosine deaminase 2 deficiency
D81.39
- Other adenosine deaminase deficiency
D81.4
- Nezelof's syndrome
D81.5
- Purine nucleoside phosphorylase [PNP] deficiency
D81.6
- Major histocompatibility complex class I deficiency
D81.7
- Major histocompatibility complex class II deficiency
D81.8
- Other combined immunodeficiencies
D81.81
- Biotin-dependent carboxylase deficiency
D81.810
- Biotinidase deficiency
D81.818
- Other biotin-dependent carboxylase deficiency
D81.819
- Biotin-dependent carboxylase deficiency, unspecified
D81.82
- Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
D81.89
- Other combined immunodeficiencies
D81.9
- Combined immunodeficiency, unspecified
Immunodeficiency associated with other major defects (D82)
D82
- Immunodeficiency associated with other major defects
D82.0
- Wiskott-Aldrich syndrome
D82.1
- Di George's syndrome
D82.2
- Immunodeficiency with short-limbed stature
D82.3
- Immunodef fol heredit defctv response to Epstein-Barr virus
D82.4
- Hyperimmunoglobulin E [IgE] syndrome
D82.8
- Immunodeficiency associated with oth major defects
D82.9
- Immunodeficiency associated with major defect, unspecified
Common variable immunodeficiency (D83)
D83
- Common variable immunodeficiency
D83.0
- Com variab immunodef w predom abnlt of B-cell nums & functn
D83.1
- Com variab immunodef w predom immunoreg T-cell disorders
D83.2
- Common variable immunodef w autoantibodies to B- or T-cells
D83.8
- Other common variable immunodeficiencies
D83.9
- Common variable immunodeficiency, unspecified
Other immunodeficiencies (D84)
D84
- Other immunodeficiencies
D84.0
- Lymphocyte function antigen-1 [LFA-1] defect
D84.1
- Defects in the complement system
D84.8
- Other specified immunodeficiencies
D84.81
- Immunodeficiency due to conditions classified elsewhere
D84.82
- Immunodeficiency due to drugs and external causes
D84.821
- Immunodeficiency due to drugs
D84.822
- Immunodeficiency due to external causes
D84.89
- Other immunodeficiencies
D84.9
- Immunodeficiency, unspecified
Sarcoidosis (D86)
D86
- Sarcoidosis
D86.0
- Sarcoidosis of lung
D86.1
- Sarcoidosis of lymph nodes
D86.2
- Sarcoidosis of lung with sarcoidosis of lymph nodes
D86.3
- Sarcoidosis of skin
D86.8
- Sarcoidosis of other sites
D86.81
- Sarcoid meningitis
D86.82
- Multiple cranial nerve palsies in sarcoidosis
D86.83
- Sarcoid iridocyclitis
D86.84
- Sarcoid pyelonephritis
D86.85
- Sarcoid myocarditis
D86.86
- Sarcoid arthropathy
D86.87
- Sarcoid myositis
D86.89
- Sarcoidosis of other sites
D86.9
- Sarcoidosis, unspecified
Other disorders involving the immune mechanism, not elsewhere classified (D89)
D89
- Oth disorders involving the immune mechanism, NEC
D89.0
- Polyclonal hypergammaglobulinemia
D89.1
- Cryoglobulinemia
D89.2
- Hypergammaglobulinemia, unspecified
D89.3
- Immune reconstitution syndrome
D89.4
- Mast cell activation syndrome and related disorders
D89.40
- Mast cell activation, unspecified
D89.41
- Monoclonal mast cell activation syndrome
D89.42
- Idiopathic mast cell activation syndrome
D89.43
- Secondary mast cell activation
D89.44
- Hereditary alpha tryptasemia
D89.49
- Other mast cell activation disorder
D89.8
- Oth disrd involving the immune mechanism, NEC
D89.81
- Graft-versus-host disease
D89.810
- Acute graft-versus-host disease
D89.811
- Chronic graft-versus-host disease
D89.812
- Acute on chronic graft-versus-host disease
D89.813
- Graft-versus-host disease, unspecified
D89.82
- Autoimmune lymphoproliferative syndrome [ALPS]
D89.83
- Cytokine release syndrome
D89.831
- Cytokine release syndrome, grade 1
D89.832
- Cytokine release syndrome, grade 2
D89.833
- Cytokine release syndrome, grade 3
D89.834
- Cytokine release syndrome, grade 4
D89.835
- Cytokine release syndrome, grade 5
D89.839
- Cytokine release syndrome, grade unspecified
D89.84
- IgG4-related disease
D89.89
- Oth disrd involving the immune mechanism, NEC
D89.9
- Disorder involving the immune mechanism, unspecified