Diagnosis Code

D58.1 HEREDITARY ELLIPTOCYTOSIS


Code Information

Diagnosis Code: D58.1

Short Description: Hereditary elliptocytosis

Long Description: Hereditary elliptocytosis

The code D58.1 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Hemolytic anemias (D55-D59)
      • Other hereditary hemolytic anemias (D58)
        • D58.1 Hereditary elliptocytosis

Code Version: 2022 ICD-10-CM


Synonyms

  • Alport syndrome, intellectual disability, midface hypoplasia, elliptocytosis syndrome
  • Congenital nephritis
  • Elliptocytosis
  • Hereditary elliptocytosis
  • Hereditary elliptocytosis
  • Hereditary elliptocytosis
  • Hereditary elliptocytosis
  • Hereditary elliptocytosis
  • Hereditary elliptocytosis
  • Hereditary elliptocytosis
  • Hereditary elliptocytosis
  • Hereditary elliptocytosis
  • Hereditary elliptocytosis due to abnormal protein 4.1
  • Hereditary elliptocytosis due to alpha spectrin defect
  • Hereditary elliptocytosis due to beta spectrin defect in self-association
  • Hereditary elliptocytosis due to beta spectrin-ankyrin interaction
  • Hereditary elliptocytosis due to deficiency of protein 4.1
  • Hereditary elliptocytosis due to glycophorin C deficiency
  • Hereditary elliptocytosis with transient poikilocytosis
  • Homozygous hereditary elliptocytosis
  • Southeast Asian ovalocytosis
  • Stomatocytosis

Diagnostic Related Group(s)

The code D58.1 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Red Blood Cell Disorders With Mcc (811)
  • Red Blood Cell Disorders Without Mcc (812)

References to Index of Diseases and Injuries

The code D58.1 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Elliptocytosis (congenital)
    • Ovalocytosis (congenital) (hereditary)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D58.1 Right Arrow 282.1 Heredit elliptocytosis

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D58 Other hereditary hemolytic anemias
D58.0 Hereditary spherocytosis
D58.2 Other hemoglobinopathies
D58.8 Other specified hereditary hemolytic anemias
D58.9 Hereditary hemolytic anemia, unspecified


This page was last updated on: 10/1/2023