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Taxonomy Codes
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Hemolytic anemias (D55-D59)
Anemia due to enzyme disorders (D55)
D55
- Anemia due to enzyme disorders
D55.0
- Anemia due to glucose-6-phosphate dehydrogenase deficiency
D55.1
- Anemia due to other disorders of glutathione metabolism
D55.2
- Anemia due to disorders of glycolytic enzymes
D55.21
- Anemia due to pyruvate kinase deficiency
D55.29
- Anemia due to other disorders of glycolytic enzymes
D55.3
- Anemia due to disorders of nucleotide metabolism
D55.8
- Other anemias due to enzyme disorders
D55.9
- Anemia due to enzyme disorder, unspecified
Thalassemia (D56)
D56
- Thalassemia
D56.0
- Alpha thalassemia
D56.1
- Beta thalassemia
D56.2
- Delta-beta thalassemia
D56.3
- Thalassemia minor
D56.4
- Hereditary persistence of fetal hemoglobin [HPFH]
D56.5
- Hemoglobin E-beta thalassemia
D56.8
- Other thalassemias
D56.9
- Thalassemia, unspecified
Sickle-cell disorders (D57)
D57
- Sickle-cell disorders
D57.0
- Hb-SS disease with crisis
D57.00
- Hb-SS disease with crisis, unspecified
D57.01
- Hb-SS disease with acute chest syndrome
D57.02
- Hb-SS disease with splenic sequestration
D57.03
- Hb-SS disease with cerebral vascular involvement
D57.04
- Hb-SS disease with dactylitis
D57.09
- Hb-SS disease with crisis with other specified complication
D57.1
- Sickle-cell disease without crisis
D57.2
- Sickle-cell/Hb-C disease
D57.20
- Sickle-cell/Hb-C disease without crisis
D57.21
- Sickle-cell/Hb-C disease with crisis
D57.211
- Sickle-cell/Hb-C disease with acute chest syndrome
D57.212
- Sickle-cell/Hb-C disease with splenic sequestration
D57.213
- Sickle-cell/Hb-C disease with cerebral vascular involvement
D57.214
- Sickle-cell/Hb-C disease with dactylitis
D57.218
- Sickle-cell/Hb-C disease with crisis with oth complication
D57.219
- Sickle-cell/Hb-C disease with crisis, unspecified
D57.3
- Sickle-cell trait
D57.4
- Sickle-cell thalassemia
D57.40
- Sickle-cell thalassemia without crisis
D57.41
- Sickle-cell thalassemia, unspecified, with crisis
D57.411
- Sickle-cell thalassemia, unsp, with acute chest syndrome
D57.412
- Sickle-cell thalassemia, unsp, with splenic sequestration
D57.413
- Sickle-cell thalassemia, unsp, with cerebral vascular invl
D57.414
- Sickle-cell thalassemia, unspecified, with dactylitis
D57.418
- Sickle-cell thalassemia, unsp, with crisis with oth comp
D57.419
- Sickle-cell thalassemia, unspecified, with crisis
D57.42
- Sickle-cell thalassemia beta zero without crisis
D57.43
- Sickle-cell thalassemia beta zero with crisis
D57.431
- Sickle-cell thalassemia beta zero with acute chest syndrome
D57.432
- Sickle-cell thalassemia beta zero with splenic sequestration
D57.433
- Sickle-cell thalassemia beta zero with cereb vascular invl
D57.434
- Sickle-cell thalassemia beta zero with dactylitis
D57.438
- Sickle-cell thalassemia beta zero with crisis with oth comp
D57.439
- Sickle-cell thalassemia beta zero with crisis, unspecified
D57.44
- Sickle-cell thalassemia beta plus without crisis
D57.45
- Sickle-cell thalassemia beta plus with crisis
D57.451
- Sickle-cell thalassemia beta plus with acute chest syndrome
D57.452
- Sickle-cell thalassemia beta plus with splenic sequestration
D57.453
- Sickle-cell thalassemia beta plus with cereb vascular invl
D57.454
- Sickle-cell thalassemia beta plus with dactylitis
D57.458
- Sickle-cell thalassemia beta plus with crisis with oth comp
D57.459
- Sickle-cell thalassemia beta plus with crisis, unspecified
D57.8
- Other sickle-cell disorders
D57.80
- Other sickle-cell disorders without crisis
D57.81
- Other sickle-cell disorders with crisis
D57.811
- Other sickle-cell disorders with acute chest syndrome
D57.812
- Other sickle-cell disorders with splenic sequestration
D57.813
- Other sickle-cell disorders with cerebral vascular invl
D57.814
- Other sickle-cell disorders with dactylitis
D57.818
- Other sickle-cell disorders with crisis with oth comp
D57.819
- Other sickle-cell disorders with crisis, unspecified
Other hereditary hemolytic anemias (D58)
D58
- Other hereditary hemolytic anemias
D58.0
- Hereditary spherocytosis
D58.1
- Hereditary elliptocytosis
D58.2
- Other hemoglobinopathies
D58.8
- Other specified hereditary hemolytic anemias
D58.9
- Hereditary hemolytic anemia, unspecified
Acquired hemolytic anemia (D59)
D59
- Acquired hemolytic anemia
D59.0
- Drug-induced autoimmune hemolytic anemia
D59.1
- Other autoimmune hemolytic anemias
D59.10
- Autoimmune hemolytic anemia, unspecified
D59.11
- Warm autoimmune hemolytic anemia
D59.12
- Cold autoimmune hemolytic anemia
D59.13
- Mixed type autoimmune hemolytic anemia
D59.19
- Other autoimmune hemolytic anemia
D59.2
- Drug-induced nonautoimmune hemolytic anemia
D59.3
- Hemolytic-uremic syndrome
D59.30
- Hemolytic-uremic syndrome, unspecified
D59.31
- Infection-associated hemolytic-uremic syndrome
D59.32
- Hereditary hemolytic-uremic syndrome
D59.39
- Other hemolytic-uremic syndrome
D59.4
- Other nonautoimmune hemolytic anemias
D59.5
- Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]
D59.6
- Hemoglobinuria due to hemolysis from other external causes
D59.8
- Other acquired hemolytic anemias
D59.9
- Acquired hemolytic anemia, unspecified