Diagnosis Code

D59.5 PAROXYSMAL NOCTURNAL HEMOGLOBINURIA [MARCHIAFAVA-MICHELI]


Code Information

Diagnosis Code: D59.5

Short Description: Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]

Long Description: Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]

The code D59.5 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Hemolytic anemias (D55-D59)
      • Acquired hemolytic anemia (D59)
        • D59.5 Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]

Code Version: 2022 ICD-10-CM


Synonyms

  • Occlusion of microvasculature of skin caused by platelet plug
  • Occlusion of microvasculature of skin due to platelet thrombus associated with paroxysmal nocturnal hemoglobinuria
  • Paroxysmal nocturnal hemoglobinuria
  • Thrombophilia due to paroxysmal nocturnal hemoglobinuria

References to Index of Diseases and Injuries

The code D59.5 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Type 1 Excludes Notes:
    • hemoglobinuria NOS (@R82.3*)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D59.5 Right Arrow 283.2 Hemolytic hemoglobinuria

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D59 Acquired hemolytic anemia
D59.0 Drug-induced autoimmune hemolytic anemia
D59.1 Other autoimmune hemolytic anemias
D59.10 Autoimmune hemolytic anemia, unspecified
D59.11 Warm autoimmune hemolytic anemia
D59.12 Cold autoimmune hemolytic anemia
D59.13 Mixed type autoimmune hemolytic anemia
D59.19 Other autoimmune hemolytic anemia
D59.2 Drug-induced nonautoimmune hemolytic anemia
D59.3 Hemolytic-uremic syndrome
D59.30 Hemolytic-uremic syndrome, unspecified
D59.31 Infection-associated hemolytic-uremic syndrome
D59.32 Hereditary hemolytic-uremic syndrome
D59.39 Other hemolytic-uremic syndrome
D59.4 Other nonautoimmune hemolytic anemias
D59.6 Hemoglobinuria due to hemolysis from other external causes
D59.8 Other acquired hemolytic anemias
D59.9 Acquired hemolytic anemia, unspecified


This page was last updated on: 10/1/2023