Diagnosis Code

D84.1 DEFECTS IN THE COMPLEMENT SYSTEM


Code Information

Diagnosis Code: D84.1

Short Description: Defects in the complement system

Long Description: Defects in the complement system

The code D84.1 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Certain disorders involving the immune mechanism (D80-D89)
      • Other immunodeficiencies (D84)
        • D84.1 Defects in the complement system

Code Version: 2022 ICD-10-CM


Synonyms

  • Acquired angioedema due to C1 inhibitor autoantibody
  • Acquired C1 esterase inhibitor deficiency
  • Acquired C1 esterase inhibitor deficiency
  • Alternative pathway deficiency
  • Anaphylotoxin inactivator deficiency
  • Angioedema due to disorder of kinin metabolism
  • Angioedema due to disorder of kinin metabolism
  • Angioedema due to disorder of kinin metabolism
  • Angioedema due to disorder of kinin metabolism
  • Angioedema due to disorder of kinin metabolism
  • Angioedema of gingiva due to deficiency of C1 esterase inhibitor
  • Autoimmune angioedema
  • Autoimmune urticaria and/or angioedema
  • Classical complement pathway abnormality
  • Combined complement 6 and 7 deficiencies
  • Complement 1q beta chain deficiency
  • Complement 1q deficiency
  • Complement 1q dysfunction
  • Complement 1r deficiency
  • Complement 1s deficiency
  • Complement 2 deficiency
  • Complement 4 binding protein deficiency
  • Complement 4 deficiency
  • Complement 4A deficiency
  • Complement 4B deficiency
  • Complement 5 deficiency
  • Complement 5 dysfunction
  • Complement 5a inhibitor deficiency
  • Complement 6 deficiency
  • Complement 7 deficiency
  • Complement 8 alpha-gamma deficiency
  • Complement 8 beta chain deficiency
  • Complement 8 beta chain dysfunction
  • Complement 9 deficiency
  • Complement abnormality
  • Complement component 3 deficiency
  • Complement component 8 deficiency
  • Complement component deficiency
  • Complement deficiency disease
  • Complement receptor 1 deficiency
  • Complement receptor 3 deficiency
  • Complement receptor deficiency
  • Complement regulatory factor defect
  • Coombs negative hemolytic anemia
  • Cutis laxa with complement deficiency
  • Cutis laxa, acquired type
  • Decay accelerating factor deficiency
  • Disorder of complement
  • Edema of oral soft tissues
  • Factor B deficiency
  • Factor D deficiency
  • Factor H deficiency
  • Familial C3B inhibitor deficiency syndrome
  • Gingival edema
  • Glomerular disease due to complement system disorder
  • Hereditary angioedema
  • Hereditary angioedema with C1Inh deficiency
  • Hereditary C1 esterase inhibitor deficiency - deficient factor
  • Hereditary C1 esterase inhibitor deficiency - dysfunctional factor
  • Homologous restriction factor deficiency
  • Immunodeficiency due to MASP-2 deficiency
  • Panniculitis due to immunological disorder
  • Panniculitis with complement deficiency
  • Primary CD59 deficiency
  • Properdin deficiency disease
  • Recurrent bacterial infection
  • Recurrent Neisseria infection due to factor D deficiency
  • Terminal component deficiency

References to Index of Diseases and Injuries

The code D84.1 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • C1 esterase inhibitor [C1-INH] deficiency

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D84.1 Right Arrow 277.6 Defic circul enzyme NEC
279.8 Immune mechanism dis NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D84 Other immunodeficiencies
D84.0 Lymphocyte function antigen-1 [LFA-1] defect
D84.8 Other specified immunodeficiencies
D84.81 Immunodeficiency due to conditions classified elsewhere
D84.82 Immunodeficiency due to drugs and external causes
D84.821 Immunodeficiency due to drugs
D84.822 Immunodeficiency due to external causes
D84.89 Other immunodeficiencies
D84.9 Immunodeficiency, unspecified


This page was last updated on: 10/1/2023