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Diagnosis Code

E74.01 VON GIERKE DISEASE


Code Information

Diagnosis Code: E74.01

Short Description: von Gierke disease

Long Description: von Gierke disease

The code E74.01 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Other disorders of carbohydrate metabolism (E74)
        • E74.01 von Gierke disease

Code Version: 2022 ICD-10-CM


Synonyms

  • Deficiency of glucose-6-phosphatase
  • Glucose transport defect
  • Glucose-6-phosphate transport defect
  • Glycogen storage disease type Ia
  • Glycogen storage disease, hepatic form
  • Glycogen storage disease, hepatic form
  • Glycogen storage disease, hepatic form
  • Glycogen storage disease, type I

References to Index of Diseases and Injuries

The code E74.01 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Type I glycogen storage disease

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E74.01 Right Arrow 271.0 Glycogenosis

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E74 Other disorders of carbohydrate metabolism
E74.0 Glycogen storage disease
E74.00 Glycogen storage disease, unspecified
E74.02 Pompe disease
E74.03 Cori disease
E74.04 McArdle disease
E74.05 Lysosome-associated membrane protein 2 [LAMP2] deficiency
E74.09 Other glycogen storage disease
E74.1 Disorders of fructose metabolism
E74.10 Disorder of fructose metabolism, unspecified
E74.11 Essential fructosuria
E74.12 Hereditary fructose intolerance
E74.19 Other disorders of fructose metabolism
E74.2 Disorders of galactose metabolism
E74.20 Disorders of galactose metabolism, unspecified
E74.21 Galactosemia
E74.29 Other disorders of galactose metabolism
E74.3 Other disorders of intestinal carbohydrate absorption
E74.31 Sucrase-isomaltase deficiency
E74.39 Other disorders of intestinal carbohydrate absorption
E74.4 Disorders of pyruvate metabolism and gluconeogenesis
E74.8 Other specified disorders of carbohydrate metabolism
E74.81 Disorders of glucose transport, not elsewhere classified
E74.810 Glucose transporter protein type 1 deficiency
E74.818 Other disorders of glucose transport
E74.819 Disorders of glucose transport, unspecified
E74.89 Other specified disorders of carbohydrate metabolism
E74.9 Disorder of carbohydrate metabolism, unspecified

This page was last updated on: 10/1/2023

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