Diagnosis Code

E74.09 OTHER GLYCOGEN STORAGE DISEASE


Code Information

Diagnosis Code: E74.09

Short Description: Other glycogen storage disease

Long Description: Other glycogen storage disease

The code E74.09 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Other disorders of carbohydrate metabolism (E74)
        • E74.09 Other glycogen storage disease

Code Version: 2022 ICD-10-CM


Synonyms

  • Adult polyglucosan body disease
  • Cardiac glycogen phosphorylase kinase deficiency
  • Danon disease
  • Deficiency of alpha-dextrin endo-1,6-alpha-glucosidase
  • Glycogen phosphorylase kinase deficiency
  • Glycogen phosphorylase kinase deficiency
  • Glycogen phosphorylase kinase deficiency, autosomal recessive
  • Glycogen phosphorylase kinase deficiency, autosomal recessive
  • Glycogen storage disease due to aldolase A deficiency
  • Glycogen storage disease due to lactate dehydrogenase deficiency
  • Glycogen storage disease due to muscle beta-enolase deficiency
  • Glycogen storage disease due to muscle phosphorylase kinase deficiency
  • Glycogen storage disease due to muscle pyruvate kinase deficiency
  • Glycogen storage disease due to phosphoglycerate kinase 1 deficiency
  • Glycogen storage disease type IXB
  • Glycogen storage disease type VIII
  • Glycogen storage disease type X
  • Glycogen storage disease, hepatic form
  • Glycogen storage disease, hepatic form
  • Glycogen storage disease, hepatic form
  • Glycogen storage disease, hepatic form
  • Glycogen storage disease, hepatic form
  • Glycogen storage disease, muscular form
  • Glycogen storage disease, muscular form
  • Glycogen storage disease, muscular form
  • Glycogen storage disease, muscular form
  • Glycogen storage disease, type IV
  • Glycogen storage disease, type VI
  • Glycogen storage disease, type VII
  • Glycogen synthase deficiency
  • Glycogenosis with glucoaminophosphaturia
  • Hepatic and muscle glycogen phosphorylase kinase deficiency
  • Hepatic glycogen phosphorylase kinase deficiency
  • Hepatic glycogen synthase deficiency
  • Hypertrophic cardiomyopathy due to glycogen storage disease
  • Muscle and heart glycogen synthase deficiency
  • Phosphate transport defect
  • Polyglucosan body myopathy type 1
  • Polyglucosan body myopathy type 2

References to Index of Diseases and Injuries

The code E74.09 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Andersen disease
    • Glycogen storage disease, types 0, IV, VI-XI
    • Hers disease
    • Liver phosphorylase deficiency
    • Muscle phosphofructokinase deficiency
    • Tauri disease

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E74.09 Right Arrow 271.0 Glycogenosis

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E74 Other disorders of carbohydrate metabolism
E74.0 Glycogen storage disease
E74.00 Glycogen storage disease, unspecified
E74.01 von Gierke disease
E74.02 Pompe disease
E74.03 Cori disease
E74.04 McArdle disease
E74.05 Lysosome-associated membrane protein 2 [LAMP2] deficiency
E74.1 Disorders of fructose metabolism
E74.10 Disorder of fructose metabolism, unspecified
E74.11 Essential fructosuria
E74.12 Hereditary fructose intolerance
E74.19 Other disorders of fructose metabolism
E74.2 Disorders of galactose metabolism
E74.20 Disorders of galactose metabolism, unspecified
E74.21 Galactosemia
E74.29 Other disorders of galactose metabolism
E74.3 Other disorders of intestinal carbohydrate absorption
E74.31 Sucrase-isomaltase deficiency
E74.39 Other disorders of intestinal carbohydrate absorption
E74.4 Disorders of pyruvate metabolism and gluconeogenesis
E74.8 Other specified disorders of carbohydrate metabolism
E74.81 Disorders of glucose transport, not elsewhere classified
E74.810 Glucose transporter protein type 1 deficiency
E74.818 Other disorders of glucose transport
E74.819 Disorders of glucose transport, unspecified
E74.89 Other specified disorders of carbohydrate metabolism
E74.9 Disorder of carbohydrate metabolism, unspecified


This page was last updated on: 10/1/2023