Diagnosis Code

E77.1 DEFECTS IN GLYCOPROTEIN DEGRADATION


Code Information

Diagnosis Code: E77.1

Short Description: Defects in glycoprotein degradation

Long Description: Defects in glycoprotein degradation

The code E77.1 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Disorders of glycoprotein metabolism (E77)
        • E77.1 Defects in glycoprotein degradation

Code Version: 2022 ICD-10-CM


Synonyms

  • Adult fucosidosis
  • Aspartylglucosaminuria
  • Beta-D-mannosidosis
  • Combined deficiency of sialidase AND beta galactosidase
  • Dysmorphic sialidosis
  • Dysmorphic sialidosis with renal involvement
  • Dysmorphic sialidosis, congenital form
  • Dysmorphic sialidosis, infantile form
  • Dysmorphic sialidosis, juvenile form
  • Fucosidosis
  • Infantile fucosidosis
  • Juvenile fucosidosis
  • Mannosidosis
  • Mannosidosis, type I
  • Mannosidosis, type II
  • Mucolipidosis
  • Mucolipidosis
  • Mucolipidosis
  • Mucolipidosis
  • Mucolipidosis
  • Mucolipidosis
  • Mucolipidosis
  • Myoclonic disorder due to sialidosis
  • Oligosaccharidosis
  • Sialidosis
  • Sialidosis type 1

References to Index of Diseases and Injuries

The code E77.1 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Aspartylglucosaminuria
    • Fucosidosis
    • Mannosidosis
    • Sialidosis [mucolipidosis I]

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E77.1 Right Arrow 271.8 Dis carbohydr metab NEC
272.7 Lipidoses

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E77 Disorders of glycoprotein metabolism
E77.0 Defects in post-translational modification of lysosomal enzymes
E77.8 Other disorders of glycoprotein metabolism
E77.9 Disorder of glycoprotein metabolism, unspecified


This page was last updated on: 10/1/2023