Diagnosis Code

E78.6 LIPOPROTEIN DEFICIENCY


Code Information

Diagnosis Code: E78.6

Short Description: Lipoprotein deficiency

Long Description: Lipoprotein deficiency

The code E78.6 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Disorders of lipoprotein metabolism and other lipidemias (E78)
        • E78.6 Lipoprotein deficiency

Code Version: 2022 ICD-10-CM


Synonyms

  • Abetalipoproteinemia
  • Abetalipoproteinemia
  • Acanthocytosis
  • Apo A-I Giessen variant
  • Apo A-I Marburg variant
  • Apo A-I Milano variant
  • Apo A-I variant fisheye-like syndrome
  • ApoA-I Munster variant 1
  • ApoA-I Munster variant 2
  • ApoA-I Munster variant 3
  • Apolipoprotein A-I deficiency
  • Apolipoprotein A-I variant disorder
  • Ataxia co-occurrent and due to abetalipoproteinemia
  • Autonomic neuropathy due to Tangier disease
  • Chorea acanthocytosis syndrome
  • Familial hypoalphalipoproteinemia
  • Familial hypobetalipoproteinemia
  • Familial hypobetalipoproteinemia - heterozygous form
  • Familial hypobetalipoproteinemia - homozygous form
  • Familial hypolipoproteinemia
  • Familial lipoprotein deficiency
  • Fish-eye disease
  • Hereditary acanthocytosis
  • Hereditary acanthocytosis
  • High density lipoprotein below reference range
  • High density lipoprotein deficiency
  • Hypoalphalipoproteinemia
  • Hypo-beta-lipoproteinemia
  • Hypocholesterolemia
  • Hypolipoproteinemia
  • Inborn error of lipoprotein metabolism
  • Inborn error of lipoprotein metabolism
  • Inborn error of lipoprotein metabolism
  • Inborn error of lipoprotein metabolism
  • Inborn error of lipoprotein metabolism
  • Inborn error of lipoprotein metabolism
  • Lecithin cholesterol acyltransferase deficiency
  • Lipoprotein below reference range
  • Lipoprotein deficiency disorder
  • Low density lipoprotein cholesterol below reference range
  • McLeod neuroacanthocytosis syndrome
  • Ophthalmoplegia due to abetalipoproteinemia
  • Tangier disease

References to Index of Diseases and Injuries

The code E78.6 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Abetalipoproteinemia
    • Depressed HDL cholesterol
    • High-density lipoprotein deficiency
    • Hypoalphalipoproteinemia
    • Hypobetalipoproteinemia (familial)
    • Lecithin cholesterol acyltransferase deficiency
    • Tangier disease

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E78.6 Right Arrow 272.5 Lipoprotein deficiencies

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E78 Disorders of lipoprotein metabolism and other lipidemias
E78.0 Pure hypercholesterolemia
E78.00 Pure hypercholesterolemia, unspecified
E78.01 Familial hypercholesterolemia
E78.1 Pure hyperglyceridemia
E78.2 Mixed hyperlipidemia
E78.3 Hyperchylomicronemia
E78.4 Other hyperlipidemia
E78.41 Elevated Lipoprotein(a)
E78.49 Other hyperlipidemia
E78.5 Hyperlipidemia, unspecified
E78.7 Disorders of bile acid and cholesterol metabolism
E78.70 Disorder of bile acid and cholesterol metabolism, unspecified
E78.71 Barth syndrome
E78.72 Smith-Lemli-Opitz syndrome
E78.79 Other disorders of bile acid and cholesterol metabolism
E78.8 Other disorders of lipoprotein metabolism
E78.81 Lipoid dermatoarthritis
E78.89 Other lipoprotein metabolism disorders
E78.9 Disorder of lipoprotein metabolism, unspecified


This page was last updated on: 10/1/2023