Diagnosis Code

E78.89 OTHER LIPOPROTEIN METABOLISM DISORDERS


Code Information

Diagnosis Code: E78.89

Short Description: Other lipoprotein metabolism disorders

Long Description: Other lipoprotein metabolism disorders

The code E78.89 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Disorders of lipoprotein metabolism and other lipidemias (E78)
        • E78.89 Other lipoprotein metabolism disorders

Code Version: 2022 ICD-10-CM


Synonyms

  • Combined heterozygous low density lipoprotein receptor co-occurrent with low density lipoprotein receptor adaptor protein 1 mutations
  • Combined pancreatic lipase and colipase deficiency
  • Deficiency of glycerophosphocholine phosphodiesterase
  • Dyslipidemia
  • Dyslipidemia
  • Dyslipidemia due to type 2 diabetes mellitus
  • Dyslipidemia with high density lipoprotein below reference range and triglyceride above reference range due to type 2 diabetes mellitus
  • Familial disease with storage of sterols
  • Farber's lipogranulomatosis
  • Fat overload syndrome
  • GM3 synthase deficiency
  • Hepatic lipase deficiency
  • Heterozygous sitosterolemia
  • High density lipoprotein below reference range
  • Homozygous sitosterolemia
  • Hypolipidemia
  • Intestinal lipofuscinosis
  • Lipid proteinosis
  • Lipofuscinosis
  • Lipogranulomatosis subcutanea of Rothmann and Makai
  • Lipoprotein above reference range
  • Lipoprotein below reference range
  • Low density lipoprotein cholesterol above reference range
  • Low density lipoprotein receptor adaptor protein 1 mutation
  • Low density lipoprotein receptor adaptor protein 1 mutation
  • Low density lipoprotein receptor mutation
  • Low density lipoprotein receptor mutation
  • Lysosomal acid lipase deficiency
  • Male emopamil-binding protein disorder with neurological defect
  • Proteinosis
  • Sitosterolemia
  • Triglyceride level - finding

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E78.89 Right Arrow 272.8 Lipoid metabol dis NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E78 Disorders of lipoprotein metabolism and other lipidemias
E78.0 Pure hypercholesterolemia
E78.00 Pure hypercholesterolemia, unspecified
E78.01 Familial hypercholesterolemia
E78.1 Pure hyperglyceridemia
E78.2 Mixed hyperlipidemia
E78.3 Hyperchylomicronemia
E78.4 Other hyperlipidemia
E78.41 Elevated Lipoprotein(a)
E78.49 Other hyperlipidemia
E78.5 Hyperlipidemia, unspecified
E78.6 Lipoprotein deficiency
E78.7 Disorders of bile acid and cholesterol metabolism
E78.70 Disorder of bile acid and cholesterol metabolism, unspecified
E78.71 Barth syndrome
E78.72 Smith-Lemli-Opitz syndrome
E78.79 Other disorders of bile acid and cholesterol metabolism
E78.8 Other disorders of lipoprotein metabolism
E78.81 Lipoid dermatoarthritis
E78.9 Disorder of lipoprotein metabolism, unspecified


This page was last updated on: 10/1/2023