Diagnosis Code

E88.40 MITOCHONDRIAL METABOLISM DISORDER, UNSPECIFIED


Code Information

Diagnosis Code: E88.40

Short Description: Mitochondrial metabolism disorder, unspecified

Long Description: Mitochondrial metabolism disorder, unspecified

The code E88.40 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Other and unspecified metabolic disorders (E88)
        • E88.40 Mitochondrial metabolism disorder, unspecified

Code Version: 2022 ICD-10-CM


Synonyms

  • Chorea due to metabolic disorder
  • Chorea due to mitochondrial cytopathy
  • Demyelination of central nervous system co-occurrent and due to mitochondrial disease
  • Dilated cardiomyopathy due to mitochondrial disease
  • Glomerular disease due to mitochondrial cytopathy
  • Hypertrophic mitochondrial cardiomyopathy
  • Infantile hypertrophic cardiomyopathy due to MRPL44 deficiency
  • Liver disease co-occurrent and due to mitochondrial disorder
  • Mitochondrial cytopathy
  • Mitochondrial metabolism defect
  • Myoclonic disorder due to mitochondrial disorder
  • Non-syndromic mitochondrial sensorineural deafness

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E88.40 Right Arrow 277.87 Dis mitochondrial metab

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E88 Other and unspecified metabolic disorders
E88.0 Disorders of plasma-protein metabolism, not elsewhere classified
E88.01 Alpha-1-antitrypsin deficiency
E88.02 Plasminogen deficiency
E88.09 Other disorders of plasma-protein metabolism, not elsewhere classified
E88.1 Lipodystrophy, not elsewhere classified
E88.2 Lipomatosis, not elsewhere classified
E88.3 Tumor lysis syndrome
E88.4 Mitochondrial metabolism disorders
E88.41 MELAS syndrome
E88.42 MERRF syndrome
E88.43 Disorders of mitochondrial tRNA synthetases
E88.49 Other mitochondrial metabolism disorders
E88.8 Other specified metabolic disorders
E88.81 Metabolic syndrome and other insulin resistance
E88.810 Metabolic syndrome
E88.811 Insulin resistance syndrome, Type A
E88.818 Other insulin resistance
E88.819 Insulin resistance, unspecified
E88.89 Other specified metabolic disorders
E88.9 Metabolic disorder, unspecified
E88.A Wasting disease (syndrome) due to underlying condition


This page was last updated on: 10/1/2023