Diagnosis Code: E88.49

Short Description: Other mitochondrial metabolism disorders

Long Description: Other mitochondrial metabolism disorders

The code E88.49 is VALID for claim submission

Code Classification:

• Endocrine, nutritional and metabolic diseases (E00–E89)
  • Metabolic disorders (E70-E88)
    • Other and unspecified metabolic disorders (E88)
      • E88.49 Other mitochondrial metabolism disorders

Code Version: 2022 ICD-10-CM

Synonyms

• Acute hepatic failure
• Acute infantile liver failure due to synthesis defect of mitochondrial deoxyribonucleic acid encoded protein
• Combined complex deficiencies
• Combined oxidative phosphorylation defect type 11
• Combined oxidative phosphorylation defect type 13
• Combined oxidative phosphorylation defect type 14
• Combined oxidative phosphorylation defect type 15
• Combined oxidative phosphorylation defect type 17
• Combined oxidative phosphorylation defect type 2
• Combined oxidative phosphorylation defect type 21
• Combined oxidative phosphorylation defect type 23
• Combined oxidative phosphorylation defect type 24
• Combined oxidative phosphorylation defect type 25
• Combined oxidative phosphorylation defect type 26
• Combined oxidative phosphorylation defect type 27
• Combined oxidative phosphorylation defect type 28
• Combined oxidative phosphorylation defect type 29
• Combined oxidative phosphorylation defect type 30
• Combined oxidative phosphorylation defect type 4
• Combined oxidative phosphorylation defect type 5
• Combined oxidative phosphorylation defect type 7
• Combined oxidative phosphorylation defect type 8
• Combined oxidative phosphorylation defect type 9
• Combined oxidative phosphorylation deficiency type 20
• Cytochrome-c oxidase deficiency
• Cytochrome-c oxidase deficiency
• Deficiency in enzyme complexes of mitochondrial respiratory chain
• Deficiency of cytochrome-b>5< reductase
• Deficiency of mitochondrial aspartyl-tRNA synthetase
• Deficiency of mitochondrial complex III
• Deficiency of NADH dehydrogenase
• Deficiency of NADH dehydrogenase
• Deficiency of NADH dehydrogenase
• Deficiency of NADPH-ferrihemoprotein reductase
• Deficiency of NAPH cytochrome-c>2< reductase
• Deletion and duplication of mitochondrial DNA
• Depletion of mitochondrial DNA
• Disorder of mitochondrial respiratory chain complexes
• Disorder of pyruvate metabolism and mitochondrial respiratory chain
• Encephalopathy due to mitochondrial and peroxisomal fission defect
• Fatal infantile cytochrome C oxidase deficiency
• Fatal mitochondrial disease due to combined oxidative phosphorylation deficiency 3
• Generalized dystonia
• Hepatoencephalopathy due to combined oxidative phosphorylation defect type 1
• Hereditary cerebellar atrophy
• Hypertrophic cardiomyopathy and renal tubular disease due to mitochondrial DNA mutation
• Hypertrophic mitochondrial cardiomyopathy
• Hypertrophic mitochondrial cardiomyopathy
• Hypertrophic mitochondrial cardiomyopathy
• Hypertrophic mitochondrial cardiomyopathy
• Isolated ATP synthase deficiency
• Leigh syndrome due to cytochrome C oxidase deficiency
• Leigh's disease
• Leukoencephalopathy with brain stem and spinal cord involvement and high lactate syndrome
• Leukoencephalopathy, thalamus and brainstem anomalies, high lactate syndrome
• Lipoic acid synthetase deficiency
• Lipoyl transferase 1 deficiency
• Luft's hypermetabolic myopathy
• MEPAN syndrome
• Mitochondrial DNA depletion syndrome hepatocerebrorenal form
• Mitochondrial DNA depletion syndrome, hepatocerebral form due to DGUOK deficiency
• Mitochondrial hypertrophic cardiomyopathy with lactic acidosis due to MTO1 deficiency
• Mitochondrial metabolism defect
• Mitochondrial myopathy with reversible cytochrome C oxidase deficiency
• Mitochondrial phosphate carrier deficiency
• Mitochondrial respiratory chain complex I assembly gene defect
• Mitochondrial respiratory chain complex I structural subunit gene defect
• Mitochondrial respiratory chain complex II assembly gene defect
• Mitochondrial respiratory chain complex II structural subunit gene defect
• Mitochondrial respiratory chain complex III assembly gene defect
• Mitochondrial respiratory chain complex III structural subunit gene defect
• Mitochondrial respiratory chain complex IV assembly gene defect
• Mitochondrial respiratory chain complex IV structural subunit gene defect
• Multiple mitochondrial dysfunctions syndrome
• Multiple mitochondrial dysfunctions syndrome type 1
• Multiple mitochondrial dysfunctions syndrome type 2
• Multiple mitochondrial dysfunctions syndrome type 3
• Multiple mitochondrial dysfunctions syndrome type 4
• Nicotinamide adenine dinucleotide coenzyme Q reductase deficiency
• Pearson's syndrome
• QRSL1-related combined oxidative phosphorylation defect
• Succinate-coenzyme Q reductase deficiency
• Syndromic sensorineural deafness due to combined oxidative phosphorylation defect
• Thymidine kinase 2 deficiency
• Ubiquinone dehydrogenase deficiency
• WARS2-related combined oxidative phosphorylation defect

Crosswalk Information

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This page was last updated on: 10/1/2023

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