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Taxonomy Codes
E76.02 HURLER-SCHEIE SYNDROME
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ICD-10 List
E00–E89
E70-E88
E76
E76.02
Code Information
Diagnosis Code:
E76.02
Short Description:
Hurler-Scheie syndrome
Long Description:
Hurler-Scheie syndrome
Code Version:
2025 ICD-10-CM
The code E76.02 is VALID for claim submission
Code Classification
Endocrine, nutritional and metabolic diseases (E00–E89)
Metabolic disorders (E70-E88)
Disorders of glycosaminoglycan metabolism (E76)
Synonyms
Mucopolysaccharidosis, MPS-I
Mucopolysaccharidosis, MPS-I-H/S
Crosswalk Information
ICD-10 Code
ICD-9 Code
ICD-9 Description
E76.02
277.5
Mucopolysaccharidosis
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.
Similar Codes
ICD-10 Code
ICD-10 Description
E76
Disorders of glycosaminoglycan metabolism
E76.0
Mucopolysaccharidosis, type I
E76.01
Hurler's syndrome
E76.03
Scheie's syndrome
E76.1
Mucopolysaccharidosis, type II
E76.2
Other mucopolysaccharidoses
E76.21
Morquio mucopolysaccharidoses
E76.210
Morquio A mucopolysaccharidoses
E76.211
Morquio B mucopolysaccharidoses
E76.219
Morquio mucopolysaccharidoses, unspecified
E76.22
Sanfilippo mucopolysaccharidoses
E76.29
Other mucopolysaccharidoses
E76.3
Mucopolysaccharidosis, unspecified
E76.8
Other disorders of glucosaminoglycan metabolism
E76.9
Glucosaminoglycan metabolism disorder, unspecified
This page was last updated on: 10/1/2025
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