E76.1 MUCOPOLYSACCHARIDOSIS, TYPE II

Code Information

  • Diagnosis Code: E76.1
  • Short Description: Mucopolysaccharidosis, type II
  • Long Description: Mucopolysaccharidosis, type II
  • Code Version: 2025 ICD-10-CM

The code E76.1 is VALID for claim submission

Code Classification

Synonyms

  • Cerebral degeneration in Hunter's disease
  • Cerebral degeneration in mucopolysaccharidosis
  • Hunter's syndrome, mild form
  • Hunter's syndrome, severe form
  • Mucopolysaccharidosis, MPS-II

References to Index of Diseases and Injuries

The code E76.1 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Hunter's syndrome

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E76.1 Right Arrow 277.5 Mucopolysaccharidosis
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E76 Disorders of glycosaminoglycan metabolism
E76.0 Mucopolysaccharidosis, type I
E76.01 Hurler's syndrome
E76.02 Hurler-Scheie syndrome
E76.03 Scheie's syndrome
E76.2 Other mucopolysaccharidoses
E76.21 Morquio mucopolysaccharidoses
E76.210 Morquio A mucopolysaccharidoses
E76.211 Morquio B mucopolysaccharidoses
E76.219 Morquio mucopolysaccharidoses, unspecified
E76.22 Sanfilippo mucopolysaccharidoses
E76.29 Other mucopolysaccharidoses
E76.3 Mucopolysaccharidosis, unspecified
E76.8 Other disorders of glucosaminoglycan metabolism
E76.9 Glucosaminoglycan metabolism disorder, unspecified
This page was last updated on: 10/1/2025
Previous Code
Next Code