E78.019 FAMILIAL HYPERCHOLESTEROLEMIA, UNSPECIFIED

Code Information

  • Diagnosis Code: E78.019
  • Short Description: Familial hypercholesterolemia, unspecified
  • Long Description: Familial hypercholesterolemia, unspecified
  • Code Version: 2025 ICD-10-CM

The code E78.019 is VALID for claim submission

Code Classification

Synonyms

  • Familial defective apolipoprotein B-100
  • Familial hyperalphalipoproteinemia
  • Familial hypercholesterolemia
  • Familial hypercholesterolemia due to genetic defect of apolipoprotein B
  • Hyperalphalipoproteinemia
  • Hypercholesterolemia due to cholesterol 7alpha-hydroxylase deficiency
  • Synthetic defect of bile acids

References to Index of Diseases and Injuries

The code E78.019 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Familial hypercholesterolemia NOS

Similar Codes

ICD-10 Code ICD-10 Description
E78 Disorders of lipoprotein metabolism and other lipidemias
E78.0 Pure hypercholesterolemia
E78.00 Pure hypercholesterolemia, unspecified
E78.01 Familial hypercholesterolemia
E78.010 Homozygous familial hypercholesterolemia [HoFH]
E78.011 Heterozygous familial hypercholesterolemia [HeFH]
E78.1 Pure hyperglyceridemia
E78.2 Mixed hyperlipidemia
E78.3 Hyperchylomicronemia
E78.4 Other hyperlipidemia
E78.41 Elevated Lipoprotein(a)
E78.49 Other hyperlipidemia
E78.5 Hyperlipidemia, unspecified
E78.6 Lipoprotein deficiency
E78.7 Disorders of bile acid and cholesterol metabolism
E78.70 Disorder of bile acid and cholesterol metabolism, unspecified
E78.71 Barth syndrome
E78.72 Smith-Lemli-Opitz syndrome
E78.79 Other disorders of bile acid and cholesterol metabolism
E78.8 Other disorders of lipoprotein metabolism
E78.81 Lipoid dermatoarthritis
E78.89 Other lipoprotein metabolism disorders
E78.9 Disorder of lipoprotein metabolism, unspecified
This page was last updated on: 10/1/2025