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Taxonomy Codes
E80.1 PORPHYRIA CUTANEA TARDA
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ICD-10 List
E00–E89
E70-E88
E80
E80.1
Code Information
Diagnosis Code:
E80.1
Short Description:
Porphyria cutanea tarda
Long Description:
Porphyria cutanea tarda
Code Version:
2025 ICD-10-CM
The code E80.1 is VALID for claim submission
Code Classification
Endocrine, nutritional and metabolic diseases (E00–E89)
Metabolic disorders (E70-E88)
Disorders of porphyrin and bilirubin metabolism (E80)
Synonyms
Acquired porphyria cutanea tarda
Familial porphyria cutanea tarda
Hepatic porphyria
Hepatic porphyria
Hepatic porphyria
Hepatic porphyria
Hepatic porphyria
Homozygous porphyria cutanea tarda
Porphyria cutanea tarda
Sporadic porphyria cutanea tarda
Uroporphyrinogen decarboxylase deficiency
Uroporphyrinogen decarboxylase deficiency
Uroporphyrinogen decarboxylase deficiency
Uroporphyrinogen decarboxylase deficiency
Uroporphyrinogen decarboxylase deficiency
Crosswalk Information
ICD-10 Code
ICD-9 Code
ICD-9 Description
E80.1
277.1
Dis porphyrin metabolism
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.
Similar Codes
ICD-10 Code
ICD-10 Description
E80
Disorders of porphyrin and bilirubin metabolism
E80.0
Hereditary erythropoietic porphyria
E80.2
Other and unspecified porphyria
E80.20
Unspecified porphyria
E80.21
Acute intermittent (hepatic) porphyria
E80.29
Other porphyria
E80.3
Defects of catalase and peroxidase
E80.4
Gilbert syndrome
E80.5
Crigler-Najjar syndrome
E80.6
Other disorders of bilirubin metabolism
E80.7
Disorder of bilirubin metabolism, unspecified
This page was last updated on: 10/1/2025
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