E80.21 ACUTE INTERMITTENT (HEPATIC) PORPHYRIA

Code Information

  • Diagnosis Code: E80.21
  • Short Description: Acute intermittent (hepatic) porphyria
  • Long Description: Acute intermittent (hepatic) porphyria
  • Code Version: 2025 ICD-10-CM

The code E80.21 is VALID for claim submission

Code Classification

Synonyms

  • Acute intermittent porphyria
  • Homozygous acute intermittent porphyria
  • Porphobilinogen deaminase deficiency
  • Porphobilinogen deaminase deficiency

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E80.21 Right Arrow 277.1 Dis porphyrin metabolism
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E80 Disorders of porphyrin and bilirubin metabolism
E80.0 Hereditary erythropoietic porphyria
E80.1 Porphyria cutanea tarda
E80.2 Other and unspecified porphyria
E80.20 Unspecified porphyria
E80.29 Other porphyria
E80.3 Defects of catalase and peroxidase
E80.4 Gilbert syndrome
E80.5 Crigler-Najjar syndrome
E80.6 Other disorders of bilirubin metabolism
E80.7 Disorder of bilirubin metabolism, unspecified
This page was last updated on: 10/1/2025