G11.3 CEREBELLAR ATAXIA WITH DEFECTIVE DNA REPAIR

Code Information

  • Diagnosis Code: G11.3
  • Short Description: Cerebellar ataxia with defective DNA repair
  • Long Description: Cerebellar ataxia with defective DNA repair
  • Code Version: 2025 ICD-10-CM

The code G11.3 is VALID for claim submission

Code Classification

Synonyms

  • Ataxia telangiectasia variant
  • Ataxia-telangiectasia syndrome
  • Chorea due to ataxia telangiectasia syndrome
  • Chorea due to immunological disorder
  • Dystonia due to ataxia telangiectasia syndrome

References to Index of Diseases and Injuries

The code G11.3 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Ataxia telangiectasia [Louis-Bar]
  • Type 2 Excludes Notes:
    • Cockayne's syndrome (@Q87.19*)
    • other disorders of purine and pyrimidine metabolism (@E79*.-)
    • xeroderma pigmentosum (@Q82.1*)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
G11.3 Right Arrow 334.8 Spinocerebellar dis NEC
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
G11 Hereditary ataxia
G11.0 Congenital nonprogressive ataxia
G11.1 Early-onset cerebellar ataxia
G11.10 Early-onset cerebellar ataxia, unspecified
G11.11 Friedreich ataxia
G11.19 Other early-onset cerebellar ataxia
G11.2 Late-onset cerebellar ataxia
G11.4 Hereditary spastic paraplegia
G11.5 Hypomyelination - hypogonadotropic hypogonadism - hypodontia
G11.6 Leukodystrophy with vanishing white matter disease
G11.8 Other hereditary ataxias
G11.9 Hereditary ataxia, unspecified
This page was last updated on: 10/1/2025
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