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Taxonomy Codes
G11.4 HEREDITARY SPASTIC PARAPLEGIA
Home
ICD-10 List
G00–G99
G10-G14
G11
G11.4
Code Information
Diagnosis Code:
G11.4
Short Description:
Hereditary spastic paraplegia
Long Description:
Hereditary spastic paraplegia
Code Version:
2025 ICD-10-CM
The code G11.4 is VALID for claim submission
Code Classification
Diseases of the nervous system (G00–G99)
Systemic atrophies primarily affecting the central nervous system (G10-G14)
Hereditary ataxia (G11)
Synonyms
Autosomal dominant complex hereditary spastic paraplegia
Autosomal dominant distal hereditary motor neuropathy
Autosomal dominant hereditary spastic paraplegia
Autosomal dominant spastic ataxia type 1
Autosomal dominant spastic paraplegia type 10
Autosomal dominant spastic paraplegia type 12
Autosomal dominant spastic paraplegia type 13
Autosomal dominant spastic paraplegia type 17
Autosomal dominant spastic paraplegia type 19
Autosomal dominant spastic paraplegia type 29
Autosomal dominant spastic paraplegia type 3
Autosomal dominant spastic paraplegia type 31
Autosomal dominant spastic paraplegia type 36
Autosomal dominant spastic paraplegia type 37
Autosomal dominant spastic paraplegia type 38
Autosomal dominant spastic paraplegia type 4
Autosomal dominant spastic paraplegia type 41
Autosomal dominant spastic paraplegia type 42
Autosomal dominant spastic paraplegia type 6
Autosomal dominant spastic paraplegia type 73
Autosomal dominant spastic paraplegia type 8
Autosomal dominant spastic paraplegia type 9A
Autosomal dominant spastic paraplegia type 9B
Autosomal recessive cerebellar ataxia with late-onset spasticity
Autosomal recessive complex spastic paraplegia due to Kennedy pathway dysfunction
Autosomal recessive hereditary spastic paraplegia
Autosomal recessive spastic ataxia of Charlevoix-Saguenay
Autosomal recessive spastic ataxia with leukoencephalopathy
Autosomal recessive spastic ataxia, optic atrophy, dysarthria syndrome
Autosomal recessive spastic paraplegia type 11
Autosomal recessive spastic paraplegia type 14
Autosomal recessive spastic paraplegia type 15
Autosomal recessive spastic paraplegia type 18
Autosomal recessive spastic paraplegia type 21
Autosomal recessive spastic paraplegia type 23
Autosomal recessive spastic paraplegia type 24
Autosomal recessive spastic paraplegia type 25
Autosomal recessive spastic paraplegia type 26
Autosomal recessive spastic paraplegia type 27
Autosomal recessive spastic paraplegia type 28
Autosomal recessive spastic paraplegia type 32
Autosomal recessive spastic paraplegia type 35
Autosomal recessive spastic paraplegia type 39
Autosomal recessive spastic paraplegia type 43
Autosomal recessive spastic paraplegia type 44
Autosomal recessive spastic paraplegia type 45
Autosomal recessive spastic paraplegia type 46
Autosomal recessive spastic paraplegia type 48
Autosomal recessive spastic paraplegia type 53
Autosomal recessive spastic paraplegia type 54
Autosomal recessive spastic paraplegia type 55
Autosomal recessive spastic paraplegia type 56
Autosomal recessive spastic paraplegia type 57
Autosomal recessive spastic paraplegia type 58
Autosomal recessive spastic paraplegia type 59
Autosomal recessive spastic paraplegia type 5A
Autosomal recessive spastic paraplegia type 60
Autosomal recessive spastic paraplegia type 61
Autosomal recessive spastic paraplegia type 62
Autosomal recessive spastic paraplegia type 63
Autosomal recessive spastic paraplegia type 64
Autosomal recessive spastic paraplegia type 66
Autosomal recessive spastic paraplegia type 67
Autosomal recessive spastic paraplegia type 69
Autosomal recessive spastic paraplegia type 70
Autosomal recessive spastic paraplegia type 71
Autosomal recessive spastic paraplegia type 74
Autosomal recessive spastic paraplegia type 75
Autosomal recessive spastic paraplegia type 76
Autosomal recessive spastic paraplegia type 77
Autosomal recessive spastic paraplegia type 78
Autosomal recessive spastic paraplegia type 9B
Autosomal spastic paraplegia type 30
Autosomal spastic paraplegia type 72
Bedouin spastic ataxia syndrome
Bilateral lower limb ataxia
Choreoathetosis
Chronic deafness
Complicated hereditary spastic paraplegia
Congenital miosis
Constricted pupil
Disorder of glutamine metabolism
Distal spinal muscular atrophy
Dystonia due to hereditary spastic paraplegia
Early-onset progressive encephalopathy, spastic ataxia, distal spinal muscular atrophy syndrome
Early-onset spastic ataxia, myoclonic epilepsy, neuropathy syndrome
Fryns macrocephaly
Hereditary sensory and autonomic neuropathy with spastic paraplegia
Hereditary spastic paraplegia
Infantile ascending hereditary spastic paralysis
Kyphoscoliosis, lateral tongue atrophy, hereditary spastic paraplegia syndrome
Macular corneal dystrophy
Mitochondrially encoded ATP synthase membrane subunit 6-related mitochondrial disease
Motor neuron disease due to hereditary spastic paraplegia
MT-ATP6-related mitochondrial spastic paraplegia
Palmoplantar keratoderma, spastic paralysis syndrome
Parkinsonism due to hereditary spastic paraplegia
Parkinsonism due to heredodegenerative disorder
Paroxysmal choreoathetosis
Paroxysmal dystonia
Paroxysmal dystonic choreoathetosis with episodic ataxia and spasticity
Progressive muscular atrophy
Punctate palmoplantar keratoderma
Pure hereditary spastic paraplegia
Second cranial nerve finding
Second cranial nerve finding
Second cranial nerve finding
Second cranial nerve finding
Second cranial nerve finding
Second cranial nerve finding
Second cranial nerve finding
Severe intellectual disability and progressive spastic paraplegia
Spastic ataxia with congenital miosis
Spastic ataxia, dysarthria due to glutaminase deficiency
Spastic paraparesis
Spastic paraparesis and deafness
Spastic paraparesis, cataracts, speech delay syndrome
Spastic paraplegia type 7
Spastic paraplegia with Paget disease of bone syndrome
Spastic paraplegia with precocious puberty syndrome
Spastic paraplegia, facial cutaneous lesion syndrome
Spastic paraplegia, glaucoma, intellectual disability syndrome
Spastic paraplegia, intellectual disability, nystagmus, obesity syndrome
Spastic paraplegia, nephritis, deafness syndrome
Spastic paraplegia, neuropathy, poikiloderma syndrome
Spastic paraplegia, optic atrophy, neuropathy syndrome
Spastic paraplegia, severe developmental delay, epilepsy syndrome
SPOAN and SPOAN-related disorder
SPOAN and SPOAN-related disorder
SPOAN and SPOAN-related disorder
SPOAN and SPOAN-related disorder
SPOAN and SPOAN-related disorder
X-linked complex hereditary spastic paraplegia
X-linked hereditary spastic paraplegia
X-linked pure hereditary spastic paraplegia
X-linked spastic paraplegia type 16
X-linked spastic paraplegia type 2
X-linked spastic paraplegia type 34
Crosswalk Information
ICD-10 Code
ICD-9 Code
ICD-9 Description
G11.4
334.1
Hered spastic paraplegia
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.
Similar Codes
ICD-10 Code
ICD-10 Description
G11
Hereditary ataxia
G11.0
Congenital nonprogressive ataxia
G11.1
Early-onset cerebellar ataxia
G11.10
Early-onset cerebellar ataxia, unspecified
G11.11
Friedreich ataxia
G11.19
Other early-onset cerebellar ataxia
G11.2
Late-onset cerebellar ataxia
G11.3
Cerebellar ataxia with defective DNA repair
G11.5
Hypomyelination - hypogonadotropic hypogonadism - hypodontia
G11.6
Leukodystrophy with vanishing white matter disease
G11.8
Other hereditary ataxias
G11.9
Hereditary ataxia, unspecified
This page was last updated on: 10/1/2025
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