Q04.2 HOLOPROSENCEPHALY

Code Information

  • Diagnosis Code: Q04.2
  • Short Description: Holoprosencephaly
  • Long Description: Holoprosencephaly
  • Code Version: 2025 ICD-10-CM

The code Q04.2 is VALID for claim submission

Code Classification

Synonyms

  • Agenesis of pancreas
  • Agnathia, holoprosencephaly, situs inversus syndrome
  • Alobar holoprosencephaly
  • Aplasia of pancreas
  • Cebocephaly
  • Congenital absence of pancreas
  • Congenital stenosis of nasal pyriform aperture
  • Hartsfield syndrome
  • Holoprosencephaly and postaxial polydactyly syndrome
  • Holoprosencephaly craniosynostosis syndrome
  • Holoprosencephaly sequence
  • Holoprosencephaly with caudal dysgenesis syndrome
  • Holoprosencephaly with nasal pyriformis aperture
  • Kundrat's syndrome
  • Lobar holoprosencephaly
  • Microform holoprosencephaly
  • Middle interhemispheric variant of holoprosencephaly
  • Morse Rawnsley Sargent syndrome
  • Pancreatic agenesis, holoprosencephaly syndrome
  • Semi-lobar holoprosencephaly

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q04.2 Right Arrow 742.2 Reduction deform, brain
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q04 Other congenital malformations of brain
Q04.0 Congenital malformations of corpus callosum
Q04.1 Arhinencephaly
Q04.3 Other reduction deformities of brain
Q04.4 Septo-optic dysplasia of brain
Q04.5 Megalencephaly
Q04.6 Congenital cerebral cysts
Q04.8 Other specified congenital malformations of brain
Q04.9 Congenital malformation of brain, unspecified
This page was last updated on: 10/1/2025
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