Q04.8 OTHER SPECIFIED CONGENITAL MALFORMATIONS OF BRAIN

Code Information

  • Diagnosis Code: Q04.8
  • Short Description: Other specified congenital malformations of brain
  • Long Description: Other specified congenital malformations of brain
  • Code Version: 2025 ICD-10-CM

The code Q04.8 is VALID for claim submission

Code Classification

Synonyms

  • 3C syndrome
  • Abnormality of neurogenesis
  • Abnormality of neurogenesis
  • Aprosencephaly
  • Aprosencephaly cerebellar dysgenesis
  • Aprosencephaly/atelencephaly spectrum
  • Aprosencephaly/atelencephaly spectrum
  • Athabaskan brainstem dysgenesis syndrome
  • CEDNIK syndrome
  • Central bilateral macrogyria
  • Cerebellar cortical dysplasia
  • Cerebellar hemangioblastomatosis
  • Cerebral ventriculomegaly, cystic kidney disease
  • Cerebro-facio-thoracic dysplasia
  • Chiari malformation
  • Chiari malformation type IV
  • Coffin-Siris syndrome
  • Colpocephaly
  • Communicating hydrocephalus co-occurrent and due to congenital agenesis of arachnoid villi
  • Congenital abnormal shape of cerebellum
  • Congenital abnormal shape of cerebrum
  • Congenital aniridia
  • Congenital dysplasia of fronto-parietal cortex
  • Congenital enlargement of ventricle of brain
  • Congenital enlargement of ventricle of brain
  • Congenital intrauterine infection-like syndrome
  • Congenital malformation of the meninges
  • Congenital pseudobulbar palsy
  • Congenital sequelae of disorders
  • Congenital superior cerebellar dysplasia
  • Cortical dysplasia
  • Cortical dysplasia with hemimegalencephaly
  • Cystic malformation of posterior fossa
  • Dandy-Walker syndrome
  • Defect of telencephalic division
  • Dentate dysplasia
  • Diencephalic mesencephalic junction dysplasia
  • Ecchordosis physaliphora
  • Ectopic glial tissue
  • Ectopic gray matter
  • Ectopic gray matter in centrum ovale
  • Exencephaly
  • Focal cortical dysplasia Blumcke type III
  • Focal cortical dysplasia Blumcke type IIIa
  • Focal cortical dysplasia type I
  • Focal cortical dysplasia type Ia
  • Focal cortical dysplasia type Ib
  • Focal cortical dysplasia type II
  • Focal cortical dysplasia type IIa
  • Focal cortical dysplasia type IIb
  • Gelastic seizures with hypothalamic hamartoma
  • Gillespie syndrome
  • Hamartoma of brain
  • Hamartoma of hypothalamus
  • Infantile hemangioma
  • Isolated focal cortical dysplasia
  • Laminar heterotopia
  • Localized cortical dysplasia
  • Macrogyria
  • Macrogyria
  • MECP2 related disorder
  • Microdysgenesis
  • Nasal glial heterotopia
  • Neuronal heterotopia
  • Neuronal heterotopia
  • Neuronal heterotopia
  • Neuronal heterotopia
  • Neuronal heterotopia
  • Nodular heterotopia
  • Olivary heterotopia
  • Olive dysplasia
  • Periventricular nodular heterotopia
  • Pettigrew syndrome
  • PHACE syndrome
  • Posterior-predominant lissencephaly, broad flat pons and medulla-midline crossing defects syndrome
  • PPM-X syndrome
  • Pseudobulbar palsy
  • Subcortical nodular heterotopia
  • Subependymal nodular heterotopia
  • Tubulinopathy-associated dysgyria
  • Type 1 lissencephaly
  • Ulegyria
  • Upper motor neuron disease
  • Ventriculomegaly
  • Ventriculomegaly
  • Ventriculomegaly due to developmental anomaly

References to Index of Diseases and Injuries

The code Q04.8 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Arnold-Chiari syndrome, type IV
    • Macrogyria

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q04.8 Right Arrow 742.4 Brain anomaly NEC
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q04 Other congenital malformations of brain
Q04.0 Congenital malformations of corpus callosum
Q04.1 Arhinencephaly
Q04.2 Holoprosencephaly
Q04.3 Other reduction deformities of brain
Q04.4 Septo-optic dysplasia of brain
Q04.5 Megalencephaly
Q04.6 Congenital cerebral cysts
Q04.9 Congenital malformation of brain, unspecified
This page was last updated on: 10/1/2025