Diagnosis Code

D56.0 ALPHA THALASSEMIA


Code Information

Diagnosis Code: D56.0

Short Description: Alpha thalassemia

Long Description: Alpha thalassemia

The code D56.0 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Hemolytic anemias (D55-D59)
      • Thalassemia (D56)
        • D56.0 Alpha thalassemia

Code Version: 2022 ICD-10-CM


Synonyms

  • Acquired hemoglobin H disease
  • Alpha plus thalassemia
  • Alpha plus thalassemia deletion type
  • Alpha plus thalassemia non deletion type
  • Alpha thalassemia
  • Alpha thalassemia X-linked intellectual disability syndrome
  • Alpha zero thalassemia
  • Alpha-thalassemia intellectual disability syndrome linked to chromosome 16
  • Deletion of part of short arm of chromosome 16
  • Fetal anemia
  • Fetus with hereditary disease
  • Hemoglobin Bart's hydrops syndrome
  • Hemoglobin H constant spring thalassemia
  • Hemoglobin H disease
  • Hemoglobin Paksé disease
  • Hemoglobin Seal Rock disease
  • Homozygous alpha thalassemia
  • Hydrops fetalis
  • Sickle cell anemia with coexistent alpha-thalassemia
  • Sickle cell-hemoglobin SS disease
  • Sickle cell-thalassemia disease
  • Thalassemia with other hemoglobinopathy

References to Index of Diseases and Injuries

The code D56.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Alpha thalassemia major
    • Hemoglobin H Constant Spring
    • Hemoglobin H disease
    • Hydrops fetalis due to alpha thalassemia
    • Severe alpha thalassemia
    • Triple gene defect alpha thalassemia
  • Type 1 Excludes Notes:
    • alpha thalassemia trait or minor (@D56.3*)
    • asymptomatic alpha thalassemia (@D56.3*)
    • hydrops fetalis due to isoimmunization (@P56.0*)
    • hydrops fetalis not due to immune hemolysis (@P83.2*)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D56.0 Right Arrow 282.43 Alpha thalassemia

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D56 Thalassemia
D56.1 Beta thalassemia
D56.2 Delta-beta thalassemia
D56.3 Thalassemia minor
D56.4 Hereditary persistence of fetal hemoglobin [HPFH]
D56.5 Hemoglobin E-beta thalassemia
D56.8 Other thalassemias
D56.9 Thalassemia, unspecified


This page was last updated on: 10/1/2023