Diagnosis Code

D56.4 HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN [HPFH]


Code Information

Diagnosis Code: D56.4

Short Description: Hereditary persistence of fetal hemoglobin [HPFH]

Long Description: Hereditary persistence of fetal hemoglobin [HPFH]

The code D56.4 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Hemolytic anemias (D55-D59)
      • Thalassemia (D56)
        • D56.4 Hereditary persistence of fetal hemoglobin [HPFH]

Code Version: 2022 ICD-10-CM


Synonyms

  • A>gamma< beta^+^ HPFH AND beta^0^ thalassemia in cis
  • Beta plus thalassemia
  • Beta plus thalassemia
  • Beta plus thalassemia
  • Beta zero thalassemia
  • Delta beta thalassemia
  • Delta beta zero thalassemia
  • Hereditary persistence of fetal hemoglobin
  • Hereditary persistence of fetal hemoglobin
  • Hereditary persistence of fetal hemoglobin delta beta plus thalassemia
  • Hereditary persistence of fetal hemoglobin G gamma beta plus thalassemia
  • Hereditary persistence of fetal hemoglobin thalassemia
  • Hereditary persistence of fetal hemoglobin thalassemia
  • Hereditary persistence of fetal hemoglobin thalassemia
  • Hereditary persistence of fetal hemoglobin thalassemia
  • Hereditary persistence of fetal hemoglobin with sickle cell disease syndrome
  • HPFH A gamma beta^+^ thalassemia
  • HPFH deletion type
  • HPFH linked to beta-globulin gene cluster
  • HPFH nondeletion type
  • HPFH unlinked to beta-globulin gene cluster

Diagnostic Related Group(s)

The code D56.4 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Red Blood Cell Disorders With Mcc (811)
  • Red Blood Cell Disorders Without Mcc (812)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D56.4 Right Arrow 282.7 Hemoglobinopathies NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D56 Thalassemia
D56.0 Alpha thalassemia
D56.1 Beta thalassemia
D56.2 Delta-beta thalassemia
D56.3 Thalassemia minor
D56.5 Hemoglobin E-beta thalassemia
D56.8 Other thalassemias
D56.9 Thalassemia, unspecified


This page was last updated on: 10/1/2023