Diagnosis Code

D66 HEREDITARY FACTOR VIII DEFICIENCY


Code Information

Diagnosis Code: D66

Short Description: Hereditary factor VIII deficiency

Long Description: Hereditary factor VIII deficiency

The code D66 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
      • Hereditary factor VIII deficiency (D66)
        • D66 Hereditary factor VIII deficiency

Code Version: 2022 ICD-10-CM


Synonyms

  • Combined deficiency of factor V and factor VIII
  • Factor V deficiency
  • Factor VIII deficiency
  • Hemophilia
  • Hereditary combined coagulation factor deficiency
  • Hereditary factor VIII deficiency disease
  • Hereditary factor VIII deficiency disease with inhibitor
  • Hereditary factor VIII deficiency disease without inhibitor
  • Lamellar ichthyosis
  • Mild hereditary factor VIII deficiency disease
  • Mild hereditary factor VIII deficiency disease with inhibitor
  • Mild hereditary factor VIII deficiency disease without inhibitor
  • Moderate hereditary factor VIII deficiency disease
  • Moderate hereditary factor VIII deficiency disease with inhibitor
  • Moderate hereditary factor VIII deficiency disease without inhibitor
  • Multiple sclerosis, ichthyosis, factor VIII deficiency syndrome
  • Severe hereditary factor VIII deficiency disease
  • Severe hereditary factor VIII deficiency disease with inhibitor
  • Severe hereditary factor VIII deficiency disease without inhibitor

References to Index of Diseases and Injuries

The code D66 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Classical hemophilia
    • Deficiency factor VIII (with functional defect)
    • Hemophilia NOS
    • Hemophilia A
  • Type 1 Excludes Notes:
    • factor VIII deficiency with vascular defect (@D68.0*-)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D66 Right Arrow 286.0 Cong factor viii diord

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description


This page was last updated on: 10/1/2023