D67 HEREDITARY FACTOR IX DEFICIENCY

Code Information

  • Diagnosis Code: D67
  • Short Description: Hereditary factor IX deficiency
  • Long Description: Hereditary factor IX deficiency
  • Code Version: 2025 ICD-10-CM

The code D67 is VALID for claim submission

Code Classification

Synonyms

  • Congenital factor IX deficiency variant
  • Congenital factor IX deficiency with inhibitor
  • Congenital factor IX deficiency without inhibitor
  • Factor IX deficiency
  • Hemophilia B Leyden
  • Hereditary factor IX deficiency disease
  • Hereditary factor IX deficiency disease with inhibitor
  • Hereditary factor IX deficiency disease without inhibitor
  • Mild hereditary factor IX deficiency disease
  • Mild hereditary factor IX deficiency disease with high response inhibitor
  • Mild hereditary factor IX deficiency disease with inhibitor
  • Mild hereditary factor IX deficiency disease with low response inhibitor
  • Mild hereditary factor IX deficiency disease without inhibitor
  • Moderate hereditary factor IX deficiency disease
  • Moderate hereditary factor IX deficiency disease with high response inhibitor
  • Moderate hereditary factor IX deficiency disease with inhibitor
  • Moderate hereditary factor IX deficiency disease with low response inhibitor
  • Moderate hereditary factor IX deficiency disease without inhibitor
  • Severe hereditary factor IX deficiency disease
  • Severe hereditary factor IX deficiency disease with high response inhibitor
  • Severe hereditary factor IX deficiency disease with inhibitor
  • Severe hereditary factor IX deficiency disease with low response inhibitor
  • Severe hereditary factor IX deficiency disease without inhibitor

References to Index of Diseases and Injuries

The code D67 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Christmas disease
    • Factor IX deficiency (with functional defect)
    • Hemophilia B
    • Plasma thromboplastin component [PTC] deficiency

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D67 Right Arrow 286.1 Cong factor IX disorder
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
This page was last updated on: 10/1/2025