Diagnosis Code

D89.82 AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME [ALPS]


Code Information

Diagnosis Code: D89.82

Short Description: Autoimmune lymphoproliferative syndrome [ALPS]

Long Description: Autoimmune lymphoproliferative syndrome [ALPS]

The code D89.82 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Certain disorders involving the immune mechanism (D80-D89)
      • Oth disorders involving the immune mechanism, NEC (D89)
        • D89.82 Autoimmune lymphoproliferative syndrome [ALPS]

Code Version: 2022 ICD-10-CM


Synonyms

  • Autoimmune lymphoproliferative syndrome
  • Autoimmune lymphoproliferative syndrome
  • Autoimmune lymphoproliferative syndrome due to CTLA4 haploinsufficiency
  • Autoimmune lymphoproliferative syndrome with recurrent viral infection
  • Dianzani autoimmune lymphoproliferative disease
  • RAS-associated autoimmune leukoproliferative disease
  • STAT3-related early-onset multisystem autoimmune disease

Diagnostic Related Group(s)

The code D89.82 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Connective Tissue Disorders With Mcc (545)
  • Connective Tissue Disorders With Cc (546)
  • Connective Tissue Disorders Without Cc/mcc (547)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D89.82 Right Arrow 279.41 Autoimmun lymphprof synd

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D89 Other disorders involving the immune mechanism, not elsewhere classified
D89.0 Polyclonal hypergammaglobulinemia
D89.1 Cryoglobulinemia
D89.2 Hypergammaglobulinemia, unspecified
D89.3 Immune reconstitution syndrome
D89.4 Mast cell activation syndrome and related disorders
D89.40 Mast cell activation, unspecified
D89.41 Monoclonal mast cell activation syndrome
D89.42 Idiopathic mast cell activation syndrome
D89.43 Secondary mast cell activation
D89.44 Hereditary alpha tryptasemia
D89.49 Other mast cell activation disorder
D89.8 Other specified disorders involving the immune mechanism, not elsewhere classified
D89.81 Graft-versus-host disease
D89.810 Acute graft-versus-host disease
D89.811 Chronic graft-versus-host disease
D89.812 Acute on chronic graft-versus-host disease
D89.813 Graft-versus-host disease, unspecified
D89.83 Cytokine release syndrome
D89.831 Cytokine release syndrome, grade 1
D89.832 Cytokine release syndrome, grade 2
D89.833 Cytokine release syndrome, grade 3
D89.834 Cytokine release syndrome, grade 4
D89.835 Cytokine release syndrome, grade 5
D89.839 Cytokine release syndrome, grade unspecified
D89.84 IgG4-related disease
D89.89 Other specified disorders involving the immune mechanism, not elsewhere classified
D89.9 Disorder involving the immune mechanism, unspecified


This page was last updated on: 10/1/2023