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Taxonomy Codes
E76 DISORDERS OF GLYCOSAMINOGLYCAN METABOLISM
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ICD-10 List
E00–E89
E70-E88
E76
E76
Code Information
Diagnosis Code:
E76
Short Description:
Disorders of glycosaminoglycan metabolism
Long Description:
Disorders of glycosaminoglycan metabolism
Code Version:
2025 ICD-10-CM
The code E76 is NOT VALID for claim submission
Code Classification
Endocrine, nutritional and metabolic diseases (E00–E89)
Metabolic disorders (E70-E88)
Disorders of glycosaminoglycan metabolism (E76)
Similar Codes
ICD-10 Code
ICD-10 Description
E76.0
Mucopolysaccharidosis, type I
E76.01
Hurler's syndrome
E76.02
Hurler-Scheie syndrome
E76.03
Scheie's syndrome
E76.1
Mucopolysaccharidosis, type II
E76.2
Other mucopolysaccharidoses
E76.21
Morquio mucopolysaccharidoses
E76.210
Morquio A mucopolysaccharidoses
E76.211
Morquio B mucopolysaccharidoses
E76.219
Morquio mucopolysaccharidoses, unspecified
E76.22
Sanfilippo mucopolysaccharidoses
E76.29
Other mucopolysaccharidoses
E76.3
Mucopolysaccharidosis, unspecified
E76.8
Other disorders of glucosaminoglycan metabolism
E76.9
Glucosaminoglycan metabolism disorder, unspecified
This page was last updated on: 10/1/2024
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