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Taxonomy Codes
E76.9 GLUCOSAMINOGLYCAN METABOLISM DISORDER, UNSPECIFIED
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ICD-10 List
E00–E89
E70-E88
E76
E76.9
Code Information
Diagnosis Code:
E76.9
Short Description:
Glucosaminoglycan metabolism disorder, unspecified
Long Description:
Glucosaminoglycan metabolism disorder, unspecified
Code Version:
2025 ICD-10-CM
The code E76.9 is VALID for claim submission
Code Classification
Endocrine, nutritional and metabolic diseases (E00–E89)
Metabolic disorders (E70-E88)
Disorders of glycosaminoglycan metabolism (E76)
Synonyms
Disorder of glycosaminoglycan metabolism
Crosswalk Information
ICD-10 Code
ICD-9 Code
ICD-9 Description
E76.9
277.5
Mucopolysaccharidosis
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.
Similar Codes
ICD-10 Code
ICD-10 Description
E76
Disorders of glycosaminoglycan metabolism
E76.0
Mucopolysaccharidosis, type I
E76.01
Hurler's syndrome
E76.02
Hurler-Scheie syndrome
E76.03
Scheie's syndrome
E76.1
Mucopolysaccharidosis, type II
E76.2
Other mucopolysaccharidoses
E76.21
Morquio mucopolysaccharidoses
E76.210
Morquio A mucopolysaccharidoses
E76.211
Morquio B mucopolysaccharidoses
E76.219
Morquio mucopolysaccharidoses, unspecified
E76.22
Sanfilippo mucopolysaccharidoses
E76.29
Other mucopolysaccharidoses
E76.3
Mucopolysaccharidosis, unspecified
E76.8
Other disorders of glucosaminoglycan metabolism
This page was last updated on: 10/1/2024
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