Diagnosis Code

E77.0 DEFECTS IN POST-TRANSLATIONAL MOD OF LYSOSOMAL ENZYMES


Code Information

Diagnosis Code: E77.0

Short Description: Defects in post-translational mod of lysosomal enzymes

Long Description: Defects in post-translational modification of lysosomal enzymes

The code E77.0 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Disorders of glycoprotein metabolism (E77)
        • E77.0 Defects in post-translational mod of lysosomal enzymes

Code Version: 2022 ICD-10-CM


Synonyms

  • Defect in post-translational modification of lysosomal enzymes
  • I-cell disease
  • Mucolipidosis
  • Mucolipidosis
  • Pseudo-Hurler polydystrophy

References to Index of Diseases and Injuries

The code E77.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Mucolipidosis II [I-cell disease]
    • Mucolipidosis III [pseudo-Hurler polydystrophy]

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E77.0 Right Arrow 272.7 Lipidoses

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E77 Disorders of glycoprotein metabolism
E77.1 Defects in glycoprotein degradation
E77.8 Other disorders of glycoprotein metabolism
E77.9 Disorder of glycoprotein metabolism, unspecified


This page was last updated on: 10/1/2023