Diagnosis Code

E85.0 NON-NEUROPATHIC HEREDOFAMILIAL AMYLOIDOSIS


Code Information

Diagnosis Code: E85.0

Short Description: Non-neuropathic heredofamilial amyloidosis

Long Description: Non-neuropathic heredofamilial amyloidosis

The code E85.0 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Amyloidosis (E85)
        • E85.0 Non-neuropathic heredofamilial amyloidosis

Code Version: 2022 ICD-10-CM


Synonyms

  • Cardiac familial non-neuropathic amyloidosis
  • Cerebral non-neuropathic heredofamilial amyloidosis angiopathy
  • Familial non-neuropathic amyloidosis
  • Familial non-neuropathic amyloidosis
  • Familial non-neuropathic amyloidosis
  • Glomerular disease due to familial disease
  • Glomerular disorder due to amyloidosis
  • Glomerular disorder due to non-neuropathic heredofamilial amyloidosis

Diagnostic Related Group(s)

The code E85.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Connective Tissue Disorders With Mcc (545)
  • Connective Tissue Disorders With Cc (546)
  • Connective Tissue Disorders Without Cc/mcc (547)

References to Index of Diseases and Injuries

The code E85.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Hereditary amyloid nephropathy
  • Type 2 Excludes Notes:
    • Transthyretin-related (ATTR) familial amyloid cardiomyopathy (@E85.4*)
  • Code Also:
    • associated disorders, such as:
    • autoinflammatory syndromes (@M04*.-)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E85.0 Right Arrow 277.31 Fam Mediterranean fever

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E85 Amyloidosis
E85.1 Neuropathic heredofamilial amyloidosis
E85.2 Heredofamilial amyloidosis, unspecified
E85.3 Secondary systemic amyloidosis
E85.4 Organ-limited amyloidosis
E85.8 Other amyloidosis
E85.81 Light chain (AL) amyloidosis
E85.82 Wild-type transthyretin-related (ATTR) amyloidosis
E85.89 Other amyloidosis
E85.9 Amyloidosis, unspecified


This page was last updated on: 10/1/2023