Diagnosis Code

E76.03 SCHEIE'S SYNDROME


Code Information

Diagnosis Code: E76.03

Short Description: Scheie's syndrome

Long Description: Scheie's syndrome

The code E76.03 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Disorders of glycosaminoglycan metabolism (E76)
        • E76.03 Scheie's syndrome

Code Version: 2022 ICD-10-CM


Synonyms

  • Mucopolysaccharidosis, MPS-I
  • Mucopolysaccharidosis, MPS-I-S

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E76.03 Right Arrow 277.5 Mucopolysaccharidosis

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E76 Disorders of glycosaminoglycan metabolism
E76.0 Mucopolysaccharidosis, type I
E76.01 Hurler's syndrome
E76.02 Hurler-Scheie syndrome
E76.1 Mucopolysaccharidosis, type II
E76.2 Other mucopolysaccharidoses
E76.21 Morquio mucopolysaccharidoses
E76.210 Morquio A mucopolysaccharidoses
E76.211 Morquio B mucopolysaccharidoses
E76.219 Morquio mucopolysaccharidoses, unspecified
E76.22 Sanfilippo mucopolysaccharidoses
E76.29 Other mucopolysaccharidoses
E76.3 Mucopolysaccharidosis, unspecified
E76.8 Other disorders of glucosaminoglycan metabolism
E76.9 Glucosaminoglycan metabolism disorder, unspecified


This page was last updated on: 10/1/2023